Journal of the Korean Association of Oral and Maxillofacial Surgeons

The Korean Association of Oral and Maxillofacial Surgeons (대한구강악안면외과학회)
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Management of multiple odontogenic keratocysts associated with nevoid basal cell carcinoma syndrome: a case report of 11-year follow-up

  • Hoon-Min, Kim (Department of Oral and Maxillofacial Surgery, Ulsan University Hospital, University of Ulsan College of Medicine) ;
  • Se-Jeong, Lim (Department of Oral and Maxillofacial Surgery, Ulsan University Hospital, University of Ulsan College of Medicine) ;
  • Yeong-Cheol, Cho (Department of Oral and Maxillofacial Surgery, Ulsan University Hospital, University of Ulsan College of Medicine) ;
  • Iel-Yong, Sung (Department of Oral and Maxillofacial Surgery, Ulsan University Hospital, University of Ulsan College of Medicine) ;
  • Jang-Ho, Son (Department of Oral and Maxillofacial Surgery, Ulsan University Hospital, University of Ulsan College of Medicine)
  • Received : 2021.10.06
  • Accepted : 2021.11.15
  • Published : 2022.12.31
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Abstract

Multiple odontogenic keratocysts (OKC) are a distinguishing feature of nevoid basal cell carcinoma syndrome (NBCCS). Owing to the high recurrence rate of syndromes associated OKCs, complete surgical resection is generally recommended as a definitive treatment. Herein, we report the management of multiple OKCs with marsupialization followed by excision with peripheral ostectomy in an NBCCS patient. We then discuss lesion progression over 11 years of annual follow-ups.

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References

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