Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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A Case of Coronary Sinus Atresia with a Total Anomalous Cardiac Venous Drainage to the Left Atrium without Persistent Left Superior Vena Cava: Imaging Findings on Cardiac CT

지속성 좌상대정맥을 없이, 좌심방으로 연결되는 전관상정맥환류이상과 동반된 관상정맥동 입구폐쇄 1예: 심장전산화단층촬영 소견

  • Sang Hun Baek (Department of Radiology, Dong-A University Medical Center, Dong-A University College of Medicine) ;
  • Eun-Ju Kang (Department of Radiology, Dong-A University Medical Center, Dong-A University College of Medicine) ;
  • Ki-Nam Lee (Department of Radiology, Dong-A University Medical Center, Dong-A University College of Medicine)
  • 백상훈 (동아대학교 의과대학 동아대학교의료원 영상의학과) ;
  • 강은주 (동아대학교 의과대학 동아대학교의료원 영상의학과) ;
  • 이기남 (동아대학교 의과대학 동아대학교의료원 영상의학과)
  • Received : 2020.05.24
  • Accepted : 2020.10.29
  • Published : 2021.07.01
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Abstract

The coronary sinus (CS) is the venous drainage system of the heart. CS ostium atresia is a rarely seen cardiac malformation. Congenital atresia of the CS is usually found together with persistent left superior vena cava (LSVC) and other cardiac malformations. However, isolated congenital atresia of the CS is very rare. We present a rare case of isolated congenital atresia of the CS connecting the left atrium and coronary veins without persistent LSVC in a 58-year-old female.

관상정맥동은 심장의 정맥 배출 체계이다. 관상정맥동 입구의 폐쇄는 드문 심장 기형이다. 선천적인 관상정맥동 입구의 폐쇄는 주로 지속성 좌상대정맥을 동반하며 그 외에 다른 심장 기형과 동반되어서 나타난다. 하지만 선천적인 관상정맥동 입구의 폐쇄만 단독적으로 나타나는 경우는 아주 드물다. 이 논문에서는 58세 여성에서 발견된 지속성 좌상대정맥을 동반하지 않고, 좌심방과 심장정맥이 연결되는 선천적인 관상정맥동 입구의 폐쇄만 단독적으로 나타나는 드문 증례를 보고하고자 한다.

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References

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