Korean Journal of Head & Neck Oncology (대한두경부종양학회지)

The Korean Society for Head and Neck Oncology (대한두경부종양학회)
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Treatment of Fibrous Dysplasia of the Fronto-Orbital Area with Radical Resection and Autogenous Reconstruction Using Split Calvarial Bone Graft: A Case Report

전두-안와 구역에 발생한 섬유성 이형성증의 근치적 절제술 및 자가두개골 이식을 이용한 재건을 통한 치료: 증례보고

  • Choi, Ji-An (Department of Plastic & Reconstructive Surgery, Dong-A University School of Medicine) ;
  • Kwak, Jung-Ha (Department of Plastic & Reconstructive Surgery, Dong-A University School of Medicine) ;
  • Yoon, Chung-Min (Department of Plastic & Reconstructive Surgery, Dong-A University School of Medicine)
  • 최지안 (동아대학교 의과대학 성형외과학교실) ;
  • 곽정하 (동아대학교 의과대학 성형외과학교실) ;
  • 윤청민 (동아대학교 의과대학 성형외과학교실)
  • Received : 2021.02.23
  • Accepted : 2021.03.30
  • Published : 2021.05.31
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Abstract

Fibrous dysplasia is a bone condition characterized by the replacement of normal bone tissue and the medullary cavity by abnormal fibrous tissues. Craniofacial fibrous dysplasia causes facial asymmetry compromising the aesthetics as well as vision and hearing. A 21-year-old male visited the clinic due to vertical orbital dystopia and exophthalmos that had developed over the previous 2 months. The patient was diagnosed with a fibrous dysplasia of the frontal, ethmoid bones and superior orbital wall. By a bicoronal incision on the scalp, the radical resection of the lesions was done. After harvesting the remaining frontal bone, we did the autogenous reconstruction using split calvarial bone graft. Postoperatively, the vertical orbital dystopia and exophthalmos significantly improved. The patient is satisfied with the surgical outcomes and has not reported any recurrence.

Keywords

Acknowledgement

This study was supported by the research funds of Dong-A University.

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