Journal of the Korean Association of Oral and Maxillofacial Surgeons

The Korean Association of Oral and Maxillofacial Surgeons (대한구강악안면외과학회)
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Osteopathia striata in the mandible with cranial sclerosis: a case report and review of the literature

  • Jagtap, Rohan (Division of Oral and Maxillofacial Radiology, Department of Care Planning and Restorative Sciences, University of Mississippi Medical Center School of Dentistry) ;
  • Garrido, Michelle Briner (Division of Oral and Maxillofacial Radiology, Department of Oral and Maxillofacial Diagnostic Sciences, University of Florida College of Dentistry) ;
  • Hansen, Matthew (Division of Oral and Maxillofacial Radiology, Department of Oral and Maxillofacial Diagnostic Sciences, University of Florida College of Dentistry)
  • Received : 2020.02.28
  • Accepted : 2020.05.08
  • Published : 2021.04.30
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Abstract

Osteopathia striata with cranial sclerosis (OS-CS) is a bone dysplasia characterized by a linear striated pattern of sclerosis, especially in the long bones, and cranial sclerosis. It has variable clinical findings but distinctive radiological findings. Multiple oral and dental findings have been associated with this disease and can be seen during dental and/or medical imaging of the head and neck. Dentists and clinicians must be familiar with these signs to differentiate them from pathosis or erroneous radiographs. In the following case, we present a patient with OS-CS that presented at The University of Florida College of Dentistry with multiple craniofacial manifestations of this syndrome that were seen on a panoramic radiograph, which is one of the most commonly requested radiographs by dentists.

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References

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