Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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Botryoid Wilms Tumor in a Neonate Presenting with Fetal Hydronephrosis: A Case Report

수신증으로 발견된 신생아의 포도상의 윌름스 종양: 증례 보고

  • Chu Hyun Kim (Department of Radiology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • So-Young Yoo (Department of Radiology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Tae Yeon Jeon (Department of Radiology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Ji Hye Kim (Department of Radiology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Jung-Sun Kim (Department of Pathology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Minki Baek (Department of Urology, Samsung Medical Center, Sungkyunkwan University School of Medicine)
  • 김주현 (성균관대학교 의과대학 삼성서울병원 영상의학과) ;
  • 유소영 (성균관대학교 의과대학 삼성서울병원 영상의학과) ;
  • 전태연 (성균관대학교 의과대학 삼성서울병원 영상의학과) ;
  • 김지혜 (성균관대학교 의과대학 삼성서울병원 영상의학과) ;
  • 김정선 (성균관대학교 의과대학 삼성서울병원 병리과) ;
  • 백민기 (성균관대학교 의과대학 삼성서울병원 비뇨의학과)
  • Received : 2019.08.25
  • Accepted : 2019.09.27
  • Published : 2020.05.01
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Abstract

Botryoid Wilms tumor, a very rare variant of Wilms tumor, arises from the pelvocalyceal system, and its occurrence in the fetal or neonatal period has never been reported in the literature. Herein, we report an exceedingly rare and challenging case of botryoid Wilms tumor in a neonate who initially presented with fetal hydronephrosis. Postnatal ultrasonography revealed multiple lobulating hypoechoic masses with varying degrees of intralesional vascularity within the dilated pelvocalyceal system. To our knowedge, this is a case report of botryoid Wilms tumor of the youngest child in English literature.

포도상의 윌름스 종양은 신우에서 발생하는 윌름스 종양의 희귀한 변이형이며 태아 혹은 신생아에서 진단된 경우는 아직까지 보고된 바 없다. 저자들은 산전 초음파에서 우연히 발견된 수신증으로 내원한 신생아의 포도상의 윌름스 종양을 경험하여 이를 보고하고자 한다. 출생 후 초음파 검사에서 확장된 신우 및 신배를 채우는 다수의 소엽상의 저에코 종괴가 관찰되었고 종괴 내부는 다양한 정도의 혈류 증가 소견을 보였다. 저자들이 아는 한, 영문으로 보고된 가장 어린아이에서 발생한 윌름스 종양의 증례이다.

Keywords

Acknowledgement

This case study was approved and obtaining informed consent was waived by the Institutional Review Board of our medical center.

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