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심장초음파검사로 진단된 중증 대동맥판역류를 동반한 상행대동맥박리증 1예

A Case of Ascending Aortic Dissection with Severe Aortic Regurgitation Diagnosed by Echocardiography

  • 김성희 (대전보건대학교 임상병리과) ;
  • 이옥경 (대전보건대학교 임상병리과)
  • Kim, Sung-Hee (Department of Clinical Laboratory Science, Daejeon Health Institute of Technology) ;
  • Lee, Ok-Kyoung (Department of Clinical Laboratory Science, Daejeon Health Institute of Technology)
  • 투고 : 2020.10.07
  • 심사 : 2020.10.19
  • 발행 : 2020.12.31

초록

대동맥박리(aortic dissection)란 대동맥 내막에 미세한 파열이 발생하면 높은 대동맥 압력으로 인해 대동맥의 중막이 장축으로 찢어지면서 대동맥이 진성 내강(true lumen)과 가성 내강(false lumen)으로 분리되는 것을 말하며 사망률이 아주 높은 질환으로 빈도를 보면 남자가 여자보다 2~5배 정도 많이 발생하고, 호발하는 연령대는 50~70세 사이로 알려져 있다. 본 증례에서는 자주 발생되지 않는 젊은 30대 여자에게서 발생된 대동맥 박리증 진단을 직접 경험하였던 바 중증 대동맥판 역류증(severe aortic regurgitation)을 추적하는 과정에서 처음에는 대동맥판 탈출증(aortic valve prolapse)을 의심하였다. 이 의심된 부분을 확인하는 과정에서 상행대동맥의 내막피판 관찰을 통해 대동맥 박리증을 진단할 수 있었기에 이를 보고하는 바이다.

Aortic dissection refers to the separation of the aorta into a true and false lumen as the medial membrane of the aorta is torn along the long axis due to a high aortic pressure when a minute rupture occurs in the aortic lining. The mortality rate is very high, and aortic dissection occurs 2~5 times more in men than women. The prevalent age range is 50~70 years old. In this case, the authors experienced a diagnosis of aortic dissection that occurred in a young woman in her 30s, which does not occur frequently. In the process of tracking severe aortic regurgitation, aortic valve prolapse was initially suspected. We report this case because aortic dissection could be diagnosed by observing the intimal flap of the ascending aorta in the process of confirming this suspected part.

키워드

참고문헌

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