Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient

  • Shih, Beatrice Chia-Hui (Department of Pediatric Thoracic and Cardiovascular Surgery, Seoul National University Children's Hospital, Seoul National University College of Medicine) ;
  • Lim, Jae Hong (Department of Pediatric Thoracic and Cardiovascular Surgery, Seoul National University Children's Hospital, Seoul National University College of Medicine) ;
  • Min, Jooncheol (Department of Pediatric Thoracic and Cardiovascular Surgery, Seoul National University Children's Hospital, Seoul National University College of Medicine) ;
  • Kim, Eung Re (Department of Pediatric Thoracic and Cardiovascular Surgery, Seoul National University Children's Hospital, Seoul National University College of Medicine) ;
  • Kwak, Jae Gun (Department of Pediatric Thoracic and Cardiovascular Surgery, Seoul National University Children's Hospital, Seoul National University College of Medicine) ;
  • Kim, Woong-Han (Department of Pediatric Thoracic and Cardiovascular Surgery, Seoul National University Children's Hospital, Seoul National University College of Medicine)
  • Received : 2018.08.01
  • Accepted : 2018.12.03
  • Published : 2019.04.05
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Abstract

Shone complex is a rare congenital disorder that involves 4 obstructive lesions of the left heart, as follows: parachute mitral valve, supravalvular mitral ring, subaortic stenosis, and coarctation of the aorta. Incomplete forms with 2 or 3 of these lesions in adult patients have been rarely reported in the literature, meaning that insufficient general data exist concerning the surgical strategy and clinical follow-up. Herein, we report the case of a 31-year-old woman with a diagnosis of incomplete form of Shone complex with parachute mitral valve and coarctation of the aorta who underwent successful single-stage surgical repair.

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References

  1. Shone JD, Sellers RD, Anderson RC, Adams P Jr, Lillehei CW, Edwards JE. The developmental complex of "parachute mitral valve," supravalvular ring of left atrium, subaortic stenosis, and coarctation of aorta. Am J Cardiol 1963;11:714-25. https://doi.org/10.1016/0002-9149(63)90098-5
  2. Aslam S, Khairy P, Shohoudi A, et al. Shone complex: an under-recognized congenital heart disease with substantial morbidity in adulthood. Can J Cardiol 2017;33:253-9. https://doi.org/10.1016/j.cjca.2016.09.005
  3. Prunier F, Furber AP, Laporte J, Geslin P. Discovery of a parachute mitral valve complex (Shone's anomaly) in an adult. Echocardiography 2001;18:179-82. https://doi.org/10.1046/j.1540-8175.2001.00179.x
  4. Shehatha JS, Taha AY, Mirza AJ. Late Shone complex: a case report and literature review. J Egypt Soc Cardiothorac Surg 2018;26:133-5. https://doi.org/10.1016/j.jescts.2018.03.007
  5. St Louis JD, Bannan MM, Lutin WA, Wiles HB. Surgical strategies and outcomes in patients with Shone complex: a retrospective review. Ann Thorac Surg 2007;84:1357-62. https://doi.org/10.1016/j.athoracsur.2007.05.003
  6. Grimaldi A, Vermi AC, Ho SY, et al. Surgical outcome of partial Shone complex. Interact Cardiovasc Thorac Surg 2012;14:440-4. https://doi.org/10.1093/icvts/ivr169
  7. Connolly HM, Schaff HV, Izhar U, Dearani JA, Warnes CA, Orszulak TA. Posterior pericardial ascending-to-descending aortic bypass: an alternative surgical approach for complex coarctation of the aorta. Circulation 2001;104(12 Suppl 1):I133-7. https://doi.org/10.1161/hc37t1.094897