Journal of Cardiovascular Imaging

Korean Society of Echocardiography (한국심초음파학회)
권호 표지
DOI QR코드

DOI QR Code

Rare Case of Unileaflet Mitral Valve

  • Received : 2015.12.16
  • Accepted : 2016.05.10
  • Published : 2016.06.27
⟨ Previous Next ⟩

Abstract

Unileaflet mitral valve is the rarest of the congenital mitral valve anomalies and is usually life threatening in infancy due to severe mitral regurgitation (MR). In most asymptomatic individuals, it is mostly due to hypoplastic posterior mitral leaflet. We present a 22-year-old male with palpitations, who was found to have an echocardiogram revealing an elongated anterior mitral valve leaflet with severely hypoplastic posterior mitral valve leaflet appearing as a unileaflet mitral valve without MR. Our case is one of the 11 reported cases in the literature so far. We hereby review those cases and conclude that these patients are likely to be at risk of developing worsening MR later in their lives.

Keywords

References

  1. Espinola-Zavaleta N, Vargas-Barron J, Keirns C, Rivera G, Romero-Cardenas A, Roldan J, Attie F. Three-dimensional echocardiography in congenital malformations of the mitral valve. J Am Soc Echocardiogr 2002; 15:468-72. https://doi.org/10.1067/mje.2002.115772
  2. Bar H, Siegmund A, Wolf D, Hardt S, Katus HA, Mereles D. Prevalence of asymptomatic mitral valve malformations. Clin Res Cardiol 2009; 98:305-9. https://doi.org/10.1007/s00392-009-0004-6
  3. Bezgin T, Elveran A, Karagoz A, Canga Y, Yilmaz F. Mitral valve with a single leaflet. Turk Kardiyol Dern Ars 2014;42:80-2. https://doi.org/10.5543/tkda.2014.44380
  4. Caciolli S, Gelsomino S, Fradella G, Bevilacqua S, Favilli S, Gensini GF. Severe hypoplasia of the posterior mitral leaflet. Ann Thorac Surg 2008; 86:1978-9. https://doi.org/10.1016/j.athoracsur.2008.05.055
  5. Kanagala P, Baker S, Green L, Houghton AR. Functionally uni-leaflet mitral valves in a family: a case series. Eur J Echocardiogr 2010;11:E27.
  6. Ozkan H, Tiryakioglu O, Cetinkaya AS, Uyanik EC, Bozat T. Agenesis of the mitral posterior leaflet in elderly. Ann Thorac Surg 2014;97:319-21. https://doi.org/10.1016/j.athoracsur.2013.04.134
  7. Candan O, Guler A, Aung SM, Gecmen C, Karabay CY, Yildiz M. Uni-leaflet mitral valve. Eur J Echocardiogr 2011;12:640.

Cited by

  1. Hypoplastic posterior mitral valve leaflet: A case report and review of the literature vol.35, pp.7, 2016, https://doi.org/10.1111/echo.13898
  2. Never Too Old for a Congenital Heart Disease: A Case of a Unileaflet Mitral Valve in a 76-year-old Man vol.28, pp.1, 2016, https://doi.org/10.4250/jcvi.2019.0077
  3. Never Too Old for a Congenital Heart Disease: A Case of a Unileaflet Mitral Valve in a 76-year-old Man vol.28, pp.1, 2016, https://doi.org/10.4250/jcvi.2019.27.e46
  4. (Hypoplasia of the posterior mitral leaflet - are we familiar with it?) vol.63, pp.4, 2021, https://doi.org/10.33678/cor.2020.117