The Journal of Advanced Prosthodontics

The Korean Academy of Prosthodonitics (대한치과보철학회)
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Prosthetic management of a growing patient with Russell-Silver syndrome: a clinical report

  • Kim, Kanghyun (Department of Prosthodontics, School of Dentistry, Kyung Hee University) ;
  • Noh, Kwantae (Department of Prosthodontics, School of Dentistry, Kyung Hee University) ;
  • Paek, Janghyun (Department of Prosthodontics, School of Dentistry, Kyung Hee University) ;
  • Kwon, Kung-Rock (Department of Prosthodontics, School of Dentistry, Kyung Hee University) ;
  • Pae, Ahran (Department of Prosthodontics, School of Dentistry, Kyung Hee University)
  • Received : 2015.07.22
  • Accepted : 2015.10.02
  • Published : 2015.10.30
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Abstract

Russell-Silver syndrome (RSS) is a congenital disease characterized by short stature due to growth hormone deficiency, physical asymmetry, inverted triangular face, micrognathia, prominent forehead, and hypodontia. This case report presents a prosthetic management of a 6-year-old patient with Russell-Silver syndrome treated with overdentures on the maxilla and the mandible using the remaining primary teeth. Subsequent and comprehensive dental management considering the growth and development of a young patient will be necessary.

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References

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