Annals of Clinical Neurophysiology

The Korean Society of Clinical Neurophysiology (대한임상신경생리학회)
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A Fatal Case of Full-Blown Neuro-Behcet Disease

치명적으로 만발한 신경베체트병

  • Na, Boo Suk (Department of Neurology, College of Medicine, Kyung Hee University) ;
  • Kwon, Young Nam (Department of Neurology, College of Medicine, Kyung Hee University) ;
  • Song, Soo Jin (Department of Neurology, College of Medicine, Kyung Hee University) ;
  • Song, Jong Min (Department of Neurology, College of Medicine, Kyung Hee University) ;
  • Woo, Ho Geol (Department of Neurology, College of Medicine, Kyung Hee University) ;
  • Lee, Dokyung (Department of Neurology, College of Medicine, Kyung Hee University) ;
  • Ahn, Tae-Beom (Department of Neurology, College of Medicine, Kyung Hee University)
  • 나부석 (경희대학교 의과대학 신경과학교실) ;
  • 권영남 (경희대학교 의과대학 신경과학교실) ;
  • 송수진 (경희대학교 의과대학 신경과학교실) ;
  • 송종민 (경희대학교 의과대학 신경과학교실) ;
  • 우호걸 (경희대학교 의과대학 신경과학교실) ;
  • 이도경 (경희대학교 의과대학 신경과학교실) ;
  • 안태범 (경희대학교 의과대학 신경과학교실)
  • Received : 2014.10.21
  • Accepted : 2015.04.20
  • Published : 2015.06.30
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Abstract

We reported a 48-year-old man with Behcet disease, who presented with right hemiparesis. His first brain MRI showed multiple enhanced lesions. During the recovery, he had an episode of left 6th nerve palsy without new lesions in a follow-up MRI. Third episode was cervical myelitis, resulting in respiratory difficulty and quadriplegia without any reflexes. The myelitis was not responsive to immunotherapy. He died of respiratory failure complicated with pneumonia. This is a rare case of full-blown neuro-Behcet disease.

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References

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