DOI QR코드

DOI QR Code

Monosegmental Hepatobiliary Fibropolycystic Disease Mimicking a Mass: Report of Three Cases

  • Kwon, Jung Hyeok (Department of Radiology, Keimyung University School of Medicine, Dongsan Medical Center) ;
  • Kim, Mi Jeong (Department of Radiology, Keimyung University School of Medicine, Dongsan Medical Center) ;
  • Kim, Young Hwan (Department of Radiology, Keimyung University School of Medicine, Dongsan Medical Center) ;
  • Kang, Koo Jeong (Department of Hepatobiliary Surgery, Keimyung University School of Medicine, Dongsan Medical Center) ;
  • Kang, Yu Na (Department of Pathology, Keimyung University School of Medicine, Dongsan Medical Center) ;
  • Kwon, Sun Young (Department of Pathology, Keimyung University School of Medicine, Dongsan Medical Center)
  • 투고 : 2013.02.03
  • 심사 : 2013.09.11
  • 발행 : 2014.02.01

초록

Hepatobiliary fibropolycystic diseases are a unique group of entities involving the liver and biliary tract, which are caused by abnormal embryologic development of the ductal plates at various stages. We experienced strange hepatobiliary fibropolycystic diseases with a complex mass composed of malformed ducts and biliary cysts, which did not belong to, and were different from, previously known malformations. They were unique in imaging and histologic features. We herein report three cases of monosegmental hepatobiliary fibropolycystic disease mimicking a mass.

키워드

참고문헌

  1. Brancatelli G, Federle MP, Vilgrain V, Vullierme MP, Marin D, Lagalla R. Fibropolycystic liver disease: CT and MR imaging findings. Radiographics 2005;25:659-670 https://doi.org/10.1148/rg.253045114
  2. Levy AD, Rohrmann CA Jr, Murakata LA, Lonergan GJ. Caroli's disease: radiologic spectrum with pathologic correlation. AJR Am J Roentgenol 2002;179:1053-1057 https://doi.org/10.2214/ajr.179.4.1791053
  3. Terada T, Moriki T. Monolobar hepatobiliary fibropolycystic disease. Pathol Oncol Res 2011;17:159-165 https://doi.org/10.1007/s12253-010-9285-3
  4. Terada T, Moriki T. Monolobar ductal plate malformation disease of the liver. Pathol Int 2010;60:407-412 https://doi.org/10.1111/j.1440-1827.2010.02535.x
  5. Desmet VJ. Congenital diseases of intrahepatic bile ducts: variations on the theme "ductal plate malformation". Hepatology 1992;16:1069-1083 https://doi.org/10.1002/hep.1840160434
  6. Summerfield JA, Nagafuchi Y, Sherlock S, Cadafalch J, Scheuer PJ. Hepatobiliary fibropolycystic diseases. A clinical and histological review of 51 patients. J Hepatol 1986;2:141-156 https://doi.org/10.1016/S0168-8278(86)80073-3
  7. Veigel MC, Prescott-Focht J, Rodriguez MG, Zinati R, Shao L, Moore CA, et al. Fibropolycystic liver disease in children. Pediatr Radiol 2009;39:317-327; quiz 420-421 https://doi.org/10.1007/s00247-008-1070-z
  8. Lee HK, Park SJ, Yi BH, Lee AL, Moon JH, Chang YW. Imaging features of adult choledochal cysts: a pictorial review. Korean J Radiol 2009;10:71-80 https://doi.org/10.3348/kjr.2009.10.1.71
  9. Venkatanarasimha N, Thomas R, Armstrong EM, Shirley JF, Fox BM, Jackson SA. Imaging features of ductal plate malformations in adults. Clin Radiol 2011;66:1086-1093 https://doi.org/10.1016/j.crad.2011.05.008
  10. Choi BI, Yeon KM, Kim SH, Han MC. Caroli disease: central dot sign in CT. Radiology 1990;174:161-163 https://doi.org/10.1148/radiology.174.1.2294544

피인용 문헌

  1. RE: Communication between the Cystic Lesions of the Liver and Biliary Tree: How Can We Evaluate Efficiently and Safely? vol.15, pp.4, 2014, https://doi.org/10.3348/kjr.2014.15.4.540
  2. Malignant Transformation Arising Within Unusual and Rare Hepatic Lesions: Fibropolycystic Disease Form of Ductal Plate Malformation and Biliary Adenofibroma vol.26, pp.6, 2014, https://doi.org/10.1177/1066896918758172
  3. CONGENITAL HEPATIC FIBROSIS AND OBLITERATIVE PORTAL VENOPATHY WITHOUT PORTAL HYPERTENSION - A REVIEW OF LITERATURE BASED ON AN ASYMPTOMATIC CASE vol.55, pp.4, 2018, https://doi.org/10.1590/s0004-2803.201800000-91
  4. Congenital Cystic Lesions of the Bile Ducts: Imaging-Based Diagnosis vol.49, pp.4, 2014, https://doi.org/10.1067/j.cpradiol.2019.04.005
  5. Diffuse Versus Localized Caroli Disease: A Comparative MRCP Study vol.216, pp.6, 2014, https://doi.org/10.2214/ajr.20.23522