Maxillofacial Plastic and Reconstructive Surgery

Korean Association of Maxillofacial Plastic and Reconstructive Surgeons (대한악안면성형재건외과학회)
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Gardner Syndrome Showing Multiple Osteomas in the Jaws

  • Kim, Yongsoo (Department of Oral and Maxillofacial Surgery, School of Dentistry, Chonbuk National University) ;
  • Lee, Sun Jae (Department of Oral and Maxillofacial Surgery, School of Dentistry, Chonbuk National University) ;
  • Baek, Jin-A (Department of Oral and Maxillofacial Surgery, School of Dentistry, Chonbuk National University) ;
  • Ko, Seung-O (Department of Oral and Maxillofacial Surgery, School of Dentistry, Chonbuk National University) ;
  • Leem, Dae-Ho (Department of Oral and Maxillofacial Surgery, School of Dentistry, Chonbuk National University)
  • Received : 2013.07.29
  • Accepted : 2013.11.26
  • Published : 2013.11.30
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Abstract

Gardner syndrome, an autosomal dominant inherited condition, is a subtype of familial adenomatous polyposis. It causes lesions in bones, skin, and teeth, as well as multiple gastrointestinal polyps, which, if left untreated, become malignant. Because patients with colorectal cancer have a low survival rate, early diagnosis and treatment of Gardner syndrome is critical. Therefore, the characteristic lesions of Gardner disease that appear on the face, jaws, and oral cavity must be understood; these can be evaluated by oral and maxillofacial clinicians. This report describes a case that was diagnosed and treated earlier with the help of a routine oral and maxillofacial examination and has had a seemingly good prognosis so far.

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References

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