Korean Journal of Radiology

  • 제14권4호
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  • Pages.692-696
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  • 2013
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  • 1229-6929(pISSN)
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  • 2005-8330(eISSN)
대한영상의학회 (The Korean Society of Radiology)
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Uncommon of the Uncommon: Malignant Perivascular Epithelioid Cell Tumor of the Lung

  • Lim, Hyun-ju (Department of Radiology and Center for Imaging, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Lee, Ho Yun (Department of Radiology and Center for Imaging, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Han, Joungho (Department of Pathology, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Choi, Yong Soo (Department of Thoracic Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Lee, Kyung Soo (Department of Radiology and Center for Imaging, Samsung Medical Center, Sungkyunkwan University School of Medicine)
  • 투고 : 2012.12.10
  • 심사 : 2013.04.11
  • 발행 : 2013.07.01
⟨ 이전 논문 다음 논문 ⟩

초록

A perivascular epithelioid cell (PEC) tumor is a rare mesenchymal tumor characterized by abundant cytoplasmic Periodic acid-Schiff positive glycogen (also called sugar tumor or clear cell tumor of the lung for this characteristic) and is mostly benign. We report a case of a 63-year-old man who presented with an enlarging mass on chest radiograph. After a thorough workup, diagnosis of malignant pulmonary PEC tumor with lung to lung metastases was established. Herein, the difficulties of diagnosis and management we confronted are described.

키워드

참고문헌

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피인용 문헌

  1. Malignant Perivascular Epithelioid Cell Neoplasm of the Mediastinum and the Lung : One Case Report vol.94, pp.22, 2013, https://doi.org/10.1097/md.0000000000000904
  2. Primary retroperitoneal perivascular epithelioid cell neoplasm: A case report vol.10, pp.1, 2013, https://doi.org/10.3892/ol.2015.3210
  3. Clear cell tumor of the lung : Two case reports and a review of the literature vol.95, pp.33, 2013, https://doi.org/10.1097/md.0000000000004492
  4. PEComa of the Uterus: A Rare Mesenchymal Tumor Displaying a ≪Snowstorm≫ Pattern at Magnetic Resonance Imaging vol.100, pp.1, 2016, https://doi.org/10.5334/jbr-btr.926
  5. Computerized Tomography and Magnetic Resonance Imaging Findings in Malignant Perivascular Epithelioid Cell Tumors of the Ovaries with Pulmonary Metastasis vol.13, pp.4, 2016, https://doi.org/10.5812/iranjradiol.34712
  6. Malignant perivascular epitheloid cell tumour (PEComa) of the lung - a rare entity vol.2, pp.1, 2013, https://doi.org/10.1515/iss-2016-0032
  7. Malignant perivascular epitheloid cell tumour (PEComa) of the lung - a rare entity vol.2, pp.1, 2013, https://doi.org/10.1515/iss-2016-0032
  8. A case report of perivascular epithelioid cell tumor of the lung: A benign tumor with intense FDG uptake vol.31, pp.5, 2013, https://doi.org/10.2995/jacsurg.31.638
  9. Malignant perivascular epithelioid cell tumor of the lung synchronous with a primary adenocarcinoma: one case report and review of the literature vol.19, pp.None, 2019, https://doi.org/10.1186/s12885-019-5383-0
  10. Endobronchial Clear-Cell Sugar Tumor vol.204, pp.12, 2013, https://doi.org/10.1164/rccm.202102-0332im