Korean Journal of Head & Neck Oncology (대한두경부종양학회지)

The Korean Society for Head and Neck Oncology (대한두경부종양학회)
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A Case of Malignant Peripheral Nerve Sheath Tumor with Hypopharyngeal Cancer

하인두암과 동반된 경부의 악성 말초 신경초종 1예

  • Lim, Sang-Ho (Depratment of Otorhinolaryngology-Head & Neck Surgery, School of Medicine, Chonbuk National University) ;
  • Lee, Kyung-Seok (Depratment of Otorhinolaryngology-Head & Neck Surgery, School of Medicine, Chonbuk National University) ;
  • Yang, Yoon-Soo (Depratment of Otorhinolaryngology-Head & Neck Surgery, School of Medicine, Chonbuk National University) ;
  • Hong, Ki-Hwan (Depratment of Otorhinolaryngology-Head & Neck Surgery, School of Medicine, Chonbuk National University)
  • 임상호 (전북대학교 의학전문대학원 이비인후-두경부외과학교실) ;
  • 이경석 (전북대학교 의학전문대학원 이비인후-두경부외과학교실) ;
  • 양윤수 (전북대학교 의학전문대학원 이비인후-두경부외과학교실) ;
  • 홍기환 (전북대학교 의학전문대학원 이비인후-두경부외과학교실)
  • Received : 2012.04.12
  • Accepted : 2012.05.08
  • Published : 2012.05.25
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Abstract

The malignant peripheral nerve sheath tumor(MPNST) is an extremely rare soft tissue sarcoma of ectomesenchyme also known as malignant schwannoma or malignant neurilemoma. It is a highly malignant sarcoma, which is locally invasive, frequently leading to multiple recurrences and eventual metastatic spread. The peak incidence of this disease is known to arise in the seventh decades. In human body, trunk and extremities are the most commonly involved sites, and only 8-14% of all lesions appear in head and neck region. Because immunohistochemical staining is essential in final diagnosis. The authors report a case of malignant peripheral nerve sheath tumor in neck with hypopharyngeal cancer simultaneously on a review of the literature.

Keywords

References

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