The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
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A Case of Pneumatosis Cystoides Intestinalis in a Patient with Systemic Lupus Erythematosus

전신홍반루푸스에 동반된 장기종 1예

  • Park, Jun-Won (Department of Internal Medicine, Seoul National University College of Medicine) ;
  • Song, Yeong-Wook (Department of Internal Medicine, Seoul National University College of Medicine) ;
  • Shin, Ki-Chul (Department of Internal Medicine, Seoul National University College of Medicine)
  • 박준원 (서울대학교 의과대학 내과학교실) ;
  • 송영욱 (서울대학교 의과대학 내과학교실) ;
  • 신기철 (서울대학교 의과대학 내과학교실)
  • Published : 2012.08.01
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Abstract

Pneumatosis cystoides intestinalis, which is characterized by multiple air-filled cysts in the intestinal mucosa, submucosa, and subserosa, is associated with autoimmune disorders, including systemic sclerosis, inflammatory myopathy and, rarely, systemic lupus erythematosus (SLE). Here, we report the case of a 57-year-old female with a 2-year history of SLE who developed pneumatosis cystoides intestinalis. The patient's symptoms were improved with conservative management. Although pneumatosis cystoides intestinalis is an uncommon manifestation of SLE, and follows a mainly benign course, it can be associated with vasculitis, which has a poor prognosis.

본 증례처럼 면역억제제 치료를 받고 있는 전신홍반루푸스 환자에서 복부 팽만, 복통이나 구토, 설사 등의 소화기 증상이 나타날 경우 장기종을 감별 진단에 포함시키는 것이 필요하다고 생각된다. 장기종은 흔하게 발생하는 합병증은 아니나, 혈관염을 동반하거나 고용량의 스테로이드를 장기간 사용한 환자에서 병발할 수 있으며, 대부분의 경과는 양호하여 보존적 치료만으로 호전된다. 그러나 일부 장기종의 경우 응급 수술이 필요한 장괴사나 복막염으로 진행할 수 있어 주의가 필요하다.

Keywords

References

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Cited by

  1. Pneumatosis Cystoides Intestinalis with Pneumoperitoneum Complicating Systemic Sclerosis: A Case Report vol.84, pp.6, 2013, https://doi.org/10.3904/kjm.2013.84.6.868
  2. A Case of Pneumatosis Cystoides Intestinalis in a Patient with Dermatomyositis vol.22, pp.4, 2012, https://doi.org/10.4078/jrd.2015.22.4.238