대한치과마취과학회지 (Journal of The Korean Dental Society of Anesthesiology)

  • 제11권1호
  • /
  • Pages.51-54
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  • 2011
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  • 1598-4044(pISSN)
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  • 2383-7039(eISSN)
대한치과마취과학회 (The Korean Dental Society of Anesthsiology)
권호 표지

Wolff-Hirschorn Syndrome (WHS) 환아의 치과 치료 -증례보고-

Dental Treatment of a Pediatric Patient with Wolff-Hirschorn Syndrome under General Anesthesia -A Case Report-

  • 신승우 (단국대학교 치과대학 부속 치과병원 소아치과) ;
  • 김종수 (단국대학교 치과대학 부속 치과병원 소아치과) ;
  • 김승오 (단국대학교 치과대학 부속 치과병원 치과 마취과)
  • Shin, Seung-Woo (Department of Pediatric Dentistry, School of Dentistry, Dankook University) ;
  • Kim, Jong-Soo (Department of Pediatric Dentistry, School of Dentistry, Dankook University) ;
  • Kim, Seung-Oh (Department of Dental Anesthesia, School of Dentistry, Dankook University)
  • 투고 : 2011.06.14
  • 심사 : 2011.06.21
  • 발행 : 2011.06.30
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초록

Wolff-Hirschorn syndrome is a condition that is caused by a deletion of genetic material near the end of the short (p) arm of chromosome 4. The major features of this disorder include a characteristic facial appearance, delayed growth and development, intellectual disability, and seizures. A 9-year-old girl was brought to the clinic with a chief complaint of dental examination. The child was diagnosed as WHS at Samsung medical center. The child was under Sodium valproate, Atrovastatin medication for epilepsy, hyperlipidemia and had a history of heart surgery. So prophylactic antibiotics were recommended. The child was mentally retarded and had seizure so it was difficult to manage her behavior effectively. Thus dental treatment was carried out under general anesthesia. For prompt sedation induction we used 8% sevoflurane shortly. This report presents the case of a 9-year-old girl with WHS, who has received treatment for extensive caries under general anesthesia.

키워드

참고문헌

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