The Journal of the Korean bone and joint tumor society (대한골관절종양학회지)

The Korean Musculoskeletal Tumor Society (대한근골격종양학회)
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Double Primary Presentation of Liposarcoma and Ewing's Sarcoma: A Case Report

대퇴부 지방육종 수술 후 발생한 반대측 근위 경골의 유잉육종/원시 신경 외배엽 세포종

  • Park, Hyeong-Won (Department of Orthopaedic Surgery, Chonnam National University Medical School & Hospital) ;
  • Jung, Sung-Taek (Department of Orthopaedic Surgery, Chonnam National University Medical School & Hospital) ;
  • Nah, Seon-Yoon (Department of Orthopaedic Surgery, Chonnam National University Medical School & Hospital)
  • 박형원 (전남대학교 의과대학 정형외과학교실) ;
  • 정성택 (전남대학교 의과대학 정형외과학교실) ;
  • 나선윤 (전남대학교 의과대학 정형외과학교실)
  • Received : 2011.10.29
  • Accepted : 2011.11.15
  • Published : 2011.12.30
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Abstract

The development of different entities of soft tissue sarcoma in one patient is rare. It usually affects head and neck or abdominal region, whereas those affecting the extremities are much rarer. We describe a patient with double primary presentation of liposarcoma and Ewing's sarcoma in extremity. This case implies that sarcoma patients are at increased risk of a second malignancy, and this implies a need to search for occult tumors during follow up.

악성 연부조직 종양 수술 후 이시성(metachronous)으로 발생하는 악성 골졸양은 매우 드물다. 이시성 종양은 두 경부 또는 복부에 주로 발생하며, 사지에 발생하는 경우는 더욱더 드물다. 저자들은 48세 남자환자에서 근위 대퇴부 악성 지방 육종의 광범위 변연 절제술 후 발생한 근위 경골 유잉육종/원시 신경 외배엽 세포종 1예를 경험하여 문헌 고찰과 함께 보고하는 바이다. 육종 환자들에게서는 이와 같이 이차적으로 악성 종양이 발생할 확률이 높아지기 때문에 추시 기간 동안 잠복 종양(occult tumor)에 대한 검사가 필요하겠다.

Keywords

References

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  1. Metachronous Bilateral Extremity Soft Tissue Sarcomas vol.17, pp.None, 2011, https://doi.org/10.12659/ajcr.892402