The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
권호 표지

A Case of Recurrent Kimura Disease in the Groin Area

서혜부에 재발한 기무라씨 병 1예

  • Hahn, Sung-Hwahn (Department of Internal Medicine, Dankook University College of Medicine) ;
  • Han, Jin-Hyung (Department of Internal Medicine, Dankook University College of Medicine) ;
  • Kim, Kyung-Mook (Department of Internal Medicine, Dankook University College of Medicine) ;
  • Kim, Do-Hyung (Department of Internal Medicine, Dankook University College of Medicine) ;
  • Kim, Youn-Seup (Department of Internal Medicine, Dankook University College of Medicine) ;
  • Park, Jae-Seuk (Department of Internal Medicine, Dankook University College of Medicine) ;
  • Jee, Young-Koo (Department of Internal Medicine, Dankook University College of Medicine)
  • 한성환 (단국대학교 의과대학 내과학교실) ;
  • 한진형 (단국대학교 의과대학 내과학교실) ;
  • 김경묵 (단국대학교 의과대학 내과학교실) ;
  • 김도형 (단국대학교 의과대학 내과학교실) ;
  • 김윤섭 (단국대학교 의과대학 내과학교실) ;
  • 박재석 (단국대학교 의과대학 내과학교실) ;
  • 지영구 (단국대학교 의과대학 내과학교실)
  • Published : 2011.06.01
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Abstract

Kimura disease is a rare chronic inflammatory disorder of unknown etiology, suggestive of an allergic or autoimmune mechanism, which presents mainly as soft tissue masses in the head and neck area in young Asian males. Blood tests show eosinophilia and an elevated immunoglobulin E; the typical pathologic findings are lymphoid follicular hyperplasia, interfollicular eosinophilic infiltration, and vascular hyperplasia. There is no standard treatment; surgical resection is preferred and systemic steroid or radiotherapy is used to treat disease relapses. Kimura disease in unusual sites has been reported, but there are few cases with long-term observations because of its benign nature. Here, we present the case of a female with recurrent Kimura disease; we follow her progress for about 5 years after surgical resection of masses in the right groin area, an unusual site, with a brief review of the literature.

기무라씨 병은 주로 젊은 동양인 남자에게서 다양한 부위에 무통성 종괴로 나타나지만 두경부 영역에 호발하며 양성경과를 띠는 것으로 알려져 있어 국내에서 장기적인 경과관찰이 이루어진 예가 드물다. 이에 병변의 발생이 드문 서혜부에 재발하여 수술적 절제 후 전신적으로 스테로이드를 투여하며 5년간 경과관찰 중인 여성 환자의 1예를 보고하는 바이다.

Keywords

References

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