Clinical Endoscopy

The Korean Society of Gastrointestinal Endoscopy (대한소화기내시경학회)
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Polyarteritis Nodosa Localized in Small Intestine: A Case Report

소장에 국한된 결절성 다발성 동맥염 1예

  • Lim, Byung-Hoon (Department of Internal Medicine, Seoul Veterans Hospital, Department of Pathology) ;
  • Jang, Ji-Sun (Department of Internal Medicine, Seoul Veterans Hospital, Department of Pathology) ;
  • Kim, Jung-Won (Hallym University Medical Center, Hallym University College of Medicine) ;
  • Jang, Se-Jin (Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Sung-Hoon (Department of Internal Medicine, Seoul Veterans Hospital, Department of Pathology) ;
  • Bang, Jei-So (Department of Internal Medicine, Seoul Veterans Hospital, Department of Pathology) ;
  • Yang, Soo-Hyun (Department of Internal Medicine, Seoul Veterans Hospital, Department of Pathology) ;
  • Byun, Jong-Hoon (Department of Internal Medicine, Seoul Veterans Hospital, Department of Pathology)
  • 임병훈 (서울보훈병원 소화기내과) ;
  • 장지선 (서울보훈병원 소화기내과) ;
  • 김정원 (한림대학교 의과대학 강남성심병원 병리학교실) ;
  • 장세진 (울산대학교 의과대학 서울아산병원 병리학교실) ;
  • 김성훈 (서울보훈병원 소화기내과) ;
  • 방제소 (서울보훈병원 소화기내과) ;
  • 양수현 (서울보훈병원 소화기내과) ;
  • 변종훈 (서울보훈병원 소화기내과)
  • Received : 2010.04.08
  • Accepted : 2010.07.08
  • Published : 2010.08.30
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Abstract

Polyarteritis nodosa is a systemic necrotizing vasculitis that affects mainly small and medium-sized arteries that involve multiple organs. In addition to the systemic involvement of classical vasculitis, localized vasculitis involves blood vessels within a confined vascular distribution or single organ without clinical evidence of generalized inflammation. Localized vasculitis of the gastrointestinal tract is a rare entity. In particular, a limited involvement of the small bowel is an unusual manifestation of polyarteritis nodosa. In this report, we describe a case of biopsy-proven polyarteritis nodosa presenting as small bowel bleeding without other systemic manifestations.

일반적으로 혈관염은 다발성 장기를 침범하나, 단일 장기에 발생한 국소성 혈관염이 종종 보고되었다. 그러나 소화관에 국한되어 발생한 혈관염은 매우 드물며, 소장에 발생한 국소성 혈관염은 국내에서 보고된 바 없다. 저자들은 최근 반복되는 심한 장출혈이 있어 소장 절제 수술을 시행하고 수술 후 조직 검사에서 결절성 다발성 동맥염을 진단한 증례를 경험하였다. 환자는 혈관염을 의심할 만한 전신 증상 및 다른 장기를 침범하는 검사 소견이 없어 소장에 국한된 괴사성 혈관염으로 진단하였다.

Keywords

References

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