Annals of Clinical Neurophysiology

The Korean Society of Clinical Neurophysiology (대한임상신경생리학회)
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A Case of Patulous Eustachian Tube Associated with Kennedy Disease

Kennedy병에 의한 개방성 이관 1예

  • Kim, Nam-Hee (Department of Neurology, Dongguk University Ilsan Hospital) ;
  • Cho, Chang-Gun (Department of Otorhinolaryngology-Head and Neck Surgery, Dongguk University Ilsan Hospital)
  • 김남희 (동국대학교 일산병원 신경과) ;
  • 조창건 (동국대학교 일산병원 이비인후과)
  • Received : 2010.05.14
  • Accepted : 2010.09.03
  • Published : 2010.12.31
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Abstract

We report a 53-year-old male having Kennedy disease who complained of severe bilateral tinnitus and autophony. He was diagnosed as patulous Eustachian tube based on the observation of fluttering motion of the tympanic membrane associated with respiration, which is presumed to occur secondary to bulbar weakness. The patulous Eustachian tube affected the management of his respiratory problem by impairing his ability to tolerate BiPAP. We report this rare condition with a literature review.

Keywords

References

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