Alexander씨 병 환아의 마취 관리

Anesthetic Management of a Patient with Alexander's Disease -Case Report-

  • 김범수 (영남대학교 의과대학 마취과학교실) ;
  • 지대림 (영남대학교 의과대학 마취과학교실) ;
  • 송선옥 (영남대학교 의과대학 마취과학교실)
  • Kim, Bum-Soo (Department of Anesthesiology, College of Medicine, Yeungnam University) ;
  • Jee, Dae-Lim (Department of Anesthesiology, College of Medicine, Yeungnam University) ;
  • Song, Sun-Ok (Department of Anesthesiology, College of Medicine, Yeungnam University)
  • 발행 : 2010.06.30

초록

We present here the case of a 13-year-old male patient with Alexander's disease who underwent surgical correction of a femur fracture. Alexander's disease is a rare and fatal disorder that affects the white matter in the brain and it causes developmental delay, psychomotor regression, spasticity, megaloencephaly and seizure. The patient had the possibility of a seizure attack during the perioperative period. We discuss the anesthetic management of a patient with Alexander's disease and we review the relevant literature.

키워드