Journal of the Korean Association of Oral and Maxillofacial Surgeons

The Korean Association of Oral and Maxillofacial Surgeons (대한구강악안면외과학회)
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LEIOMYOSARCOMA OF THE MAXILLARY SINUS : A CASE REPORT

상악동에 발생한 평활근 육종의 치험례

  • Choi, Se-Kyung (Department of Oral and Maxillofacial Surgery, College of Dentistry, Yonsei University) ;
  • Kim, Jae-Young (Department of Oral and Maxillofacial Surgery, College of Dentistry, Yonsei University) ;
  • Kim, So-Mi (Department of Oral and Maxillofacial Surgery, College of Dentistry, Yonsei University) ;
  • Kim, Hyun-Woo (Department of Oral and Maxillofacial Surgery, College of Dentistry, Yonsei University) ;
  • Nam, Jung-Woo (Department of Oral and Maxillofacial Surgery, College of Dentistry, Yonsei University) ;
  • Nam, Woong (Department of Oral and Maxillofacial Surgery, College of Dentistry, Yonsei University) ;
  • Cha, In-Ho (Department of Oral and Maxillofacial Surgery, College of Dentistry, Yonsei University) ;
  • Kim, Hyung-Jun (Department of Oral and Maxillofacial Surgery, College of Dentistry, Yonsei University)
  • 최세경 (연세대학교 치과대학병원 구강악안면외과) ;
  • 김재영 (연세대학교 치과대학병원 구강악안면외과) ;
  • 김소미 (연세대학교 치과대학병원 구강악안면외과) ;
  • 김현우 (연세대학교 치과대학병원 구강악안면외과) ;
  • 남정우 (연세대학교 치과대학병원 구강악안면외과) ;
  • 남웅 (연세대학교 치과대학병원 구강악안면외과) ;
  • 차인호 (연세대학교 치과대학병원 구강악안면외과) ;
  • 김형준 (연세대학교 치과대학병원 구강악안면외과)
  • Published : 2009.12.31
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Abstract

Leiomyosarcoma(LMS) is a malignant neoplasm of smooth muscle origin, which accounts for 7 % of all soft tissue sarcomas. The most common sites are the gastrointestinal tract and female genital tract. In contrast, primary LMS of the oral and maxillofacial area is rare due to the paucity of smooth muscle in this region. Especially, LMS of the paranasal sinuses is very rare and has an aggressive clinical behavior. Only 28 cases have been described in the english literature, and of these, only 3 patients treated with surgery had a disease-free survival. A 46-year-old woman came to our department for the evaluation of pain on right midface. After a diagnostic work-up, the lesion was diagnosed as LMS of the right maxillary sinus. The radical surgery was done and chemotherapy combined radiotherapy was followed from post operation 1 month. The patient was disease free at post-operation 1 year. We will report this case with literature review.

Keywords

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