Archives of Plastic Surgery

Korean Society of Plastic and Reconstructive Surgeons (대한성형외과학회)
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Orthognathic surgery in a patient with Factor VII deficiency: A Case Report

응고인자 VII 부족 환자에서의 악교정 수술: 증례보고

  • Baek, Rong Min (Department of Plastic Surgery Seoul National University Bundang Hospital) ;
  • Oh, Myung June (Department of Plastic Surgery Seoul National University Bundang Hospital) ;
  • Lee, Sang Woo (Department of Plastic Surgery Seoul National University Bundang Hospital)
  • 백롱민 (분당서울대학교병원 성형외과) ;
  • 오명준 (분당서울대학교병원 성형외과) ;
  • 이상우 (분당서울대학교병원 성형외과)
  • Published : 2009.01.15
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Abstract

Purpose: Congenital factor VII (FVII) deficiency is a rare bleeding disorder and surgery can cause excessive bleeding due to an extrinsic pathway problem. It can be diagnosed by increased PT and decreased FVII level in coagulation test. Symptom varies according to the level of FVII, but it is essential to prevent intraoperative excessive bleeding. Methods: In this report, we described the orthognatic surgery experience in a mandibular prognathism patient with congenital FVII deficiency, in which recombinant activated factor VII (rFVIIa) was used to manage the bleeding. Rsults: We could get a successful result without any complication and there was minimal intraoperative bleeding. Conclusion: The orthognathic surgery could therefore be safely performed in patients with congenital factor VII deficiency using rFVIIa.

Keywords

References

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