Abstract
Rhabdomyoma has been reported to be the most common type of cardiac tumors in fetuses and children, and multiple cardiac rhabdomyomas almost certainly signify the association with tuberous sclerosis. We report here on a case of Tetralogy of Fallot (ToF) that was associated with multiple rhabdomyomas and tuberous sclerosis. A two-year-old boy, who had undergone systemic-pulmonary shunt during the neonatal period, received total correction of his ToF after the complete regression of the cardiac tumor. The postoperative course was uneventful, and he has been follow-up for 2 months. The boy is currently in an excellent condition.
심장횡문근종은 영, 유아나 소아기에서 가장 발생 빈도가 높은 원발성 심장종양으로서, 다발성인 경우 빈번히 결절성 경화증을 동반한다. 저자들은 심장 횡문근종 및 결절성 경화증과 동반된 활로씨 사징증을 가진 환아에서 신생아기에 전신-폐 단락술을 시행하고 횡문근종이 자연적 소멸된 후 2세에 완전 교정술을 시행하여 양호한 결과를 얻었기에 보고하는 바이다.
