Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Primary Antiphospholipid Syndrome with Pulmonary Thromboembolism

폐색전증을 동반한 원발성 항인지질증후군 1예

  • Lee, Jae Beom (Department of Internal Medicine, College of Medicine, Ewha Womans University) ;
  • Sim, Yun Su (Department of Internal Medicine, College of Medicine, Ewha Womans University) ;
  • Noh, Young Wook (Department of Internal Medicine, College of Medicine, Ewha Womans University) ;
  • Park, Hye Sung (Department of Internal Medicine, College of Medicine, Ewha Womans University) ;
  • Tae, Chung Hyun (Department of Internal Medicine, College of Medicine, Ewha Womans University) ;
  • Lim, So Yeon (Department of Internal Medicine, College of Medicine, Ewha Womans University) ;
  • Jun, Yoon Hee (Department of Internal Medicine, College of Medicine, Ewha Womans University) ;
  • Ryu, Yon Ju (Department of Internal Medicine, College of Medicine, Ewha Womans University) ;
  • Chun, Eun Mi (Department of Internal Medicine, College of Medicine, Ewha Womans University) ;
  • Lee, Jin Hwa (Department of Internal Medicine, College of Medicine, Ewha Womans University) ;
  • Chang, Jung Hyun (Department of Internal Medicine, College of Medicine, Ewha Womans University) ;
  • Moon, Jin Wook (Department of Internal Medicine, College of Medicine, Ewha Womans University)
  • 이재범 (이화여자대학교 의과대학 내과학교실) ;
  • 심윤수 (이화여자대학교 의과대학 내과학교실) ;
  • 노영욱 (이화여자대학교 의과대학 내과학교실) ;
  • 박혜성 (이화여자대학교 의과대학 내과학교실) ;
  • 태정현 (이화여자대학교 의과대학 내과학교실) ;
  • 임소연 (이화여자대학교 의과대학 내과학교실) ;
  • 전윤희 (이화여자대학교 의과대학 내과학교실) ;
  • 류연주 (이화여자대학교 의과대학 내과학교실) ;
  • 천은미 (이화여자대학교 의과대학 내과학교실) ;
  • 이진화 (이화여자대학교 의과대학 내과학교실) ;
  • 장중현 (이화여자대학교 의과대학 내과학교실) ;
  • 문진욱 (이화여자대학교 의과대학 내과학교실)
  • Received : 2007.04.20
  • Accepted : 2007.06.07
  • Published : 2007.07.30
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Abstract

Antiphospholipid syndrome (APS) causes recurrent thromboses and morbidity during pregnancy, including fetal loss. This malady is associated with the persistent presence of anticardiolipin antibody or lupus anticoagulant. The pulmonary manifestations of antiphospholipid syndrome include pulmonary thromboembolism, pulmonary hypertension, acute respiratory distress syndrome, etc. Pulmonary thromboembolism is often the initial manifestation of antiphospholipid syndrome and a timely diagnosis is critical due to the high mortality rate. We herein report on a 19-year-old man with pulmonary thromboembolism that was caused by primary antiphospholipid syndrome. He presented with blood-tinged sputum, fever and epigastric pain, and his chest computerized tomography showed pulmonary thromboembolism. The other possible causes of pulmonary thromboembolism were excluded and the diagnosis of primary antiphospholipid syndrome was confirmed by the lupus anticoagulant that was present on two occasions six weeks apart. We also discuss the nature and management of antiphospholipid syndrome, along with a brief review of the relevant literatures.

저자 등은 19세 남자 환자에서 폐색전증을 동반한 원발성 항인지질증후군 증례를 경험하였기에 문헌 고찰과 함께 보고하는 바이다.

Keywords

References

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