Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Tracheomalacia Associated with Esophageal Atresia - A case report -

식도폐쇄증과 동반된 기관연화증 - 1예 보고 -

  • Song Seung-Hwan (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Pusan National University) ;
  • Chang Yun-Hee (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Pusan National University) ;
  • Lee Chang-Hun (Department of Pathology, College of Medicine, Pusan National University) ;
  • Shin Dong-Hoon (Department of Pathology, College of Medicine, Pusan National University) ;
  • Sung Si-Chan (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Pusan National University)
  • 송승환 (부산대학교 의과대학 흉부외과학교실) ;
  • 장윤희 (부산대학교 의과대학 흉부외과학교실) ;
  • 이창훈 (부산대학교 의과대학 병리학교실) ;
  • 신동훈 (부산대학교 의과대학 병리학교실) ;
  • 성시찬 (부산대학교 의과대학 흉부외과학교실)
  • Published : 2006.08.01
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Abstract

Congenital tracheomalacia associated esophageal atresia is a rare foregut anomaly. We report a case of 40-day old male infant with tracheomalacia who has undergone repair of esophageal atresia at his age of 1 day. The patient had progressive dyspnea and stridor after repair of esophageal atresia. His 3-dimensional chest computed tomography showed severe stenosis at the middle of trachea. We underwent resection and end-to-end anastomosis under cardiopulmonary bypass. Histologic examination revealed esophageal tissues indicating congenital origin as well as no cartilage.

선천적으로 발생한 식도 폐쇄증과 연관된 기관연화증은 매우 드문 기형이다. 본 증례는 생후 1일째 식도 폐쇄증 수술을 받은 환아가 기관연화증으로 진단되어 생후 40일에 교정수술을 하였다. 식도수술 후에 진행하는 호흡곤란과 천명음을 보였으며, 삼차원 컴퓨터촬영상 기관 중부에 심한 협착소견을 보였다. 심폐바이패스 하에서 협착부를 절제하고 단단 문합하였다. 조직학적 검사상 연골이 없을 뿐 아니라 식도조직을 보여 선천성 기관연화증으로 진단할 수 있었다.

Keywords

References

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