비디오흉강경을 이용하여 폐절제술로 치료한 편측 미만성 폐동정맥루 1례

A Case of Video-Assisted Thoracoscopic Pneumonectomy for Unilateral Diffuse Pulmonary Arteriovenous Malformation

  • 정종열 (연세대학교 의과대학 내과학교실) ;
  • 임종근 (연세대학교 의과대학 내과학교실) ;
  • 전성완 (연세대학교 의과대학 내과학교실) ;
  • 서원나 (연세대학교 의과대학 내과학교실) ;
  • 김대준 (연세대학교 의과대학 흉부외과학교실) ;
  • 이광훈 (연세대학교 의과대학 영상진단학과학교실) ;
  • 박무석 (연세대학교 의과대학 내과학교실) ;
  • 김세규 (연세대학교 의과대학 내과학교실) ;
  • 장준 (연세대학교 의과대학 내과학교실) ;
  • 김성규 (연세대학교 의과대학 내과학교실) ;
  • 김영삼 (연세대학교 의과대학 내과학교실)
  • Jung, Jong Yul (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Lim, Jong Keun (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Chun, Sung Wan (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Suh, Won Na (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Dae Jun (Department of Thoracic and Cardiovascular Surgery, Yonsei University College of Medicine) ;
  • Lee, Kwang Hun (Department of Diagnostic Radiology, Yonsei University College of Medicine) ;
  • Park, Moo Suk (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Se Kyu (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Chang, Joon (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Sung Kyu (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Young Sam (Department of Internal Medicine, Yonsei University College of Medicine)
  • 투고 : 2006.10.16
  • 심사 : 2006.11.06
  • 발행 : 2006.12.30

초록

저자들은 편측성으로 우측 폐전체를 침범한 미만성 폐동정맥루에 대해 색전술 등의 중재적 시술이 불가능하여 비디오흉강경을 이용해서 폐절제술로 치료한 1예를 경험하였기에, 문헌 고찰과 함께 보고하는 바이다.

Pulmonary arteriovenous malformations (PAVMs) are abnormal direct communications between the pulmonary arteries and veins. PAVMs may occur as either an isolated abnormality or in association with hereditary hemorrhagic telangiectasia, also called Osler-Weber-Rendu disease. The topic of PAVM has recently been extensively reviewed, but little is known about the clinical characteristics and course of patients having a diffuse pattern of the disease. Herein, is reported a case of unilateral diffuse PAVM in an 18 year old female patient, who underwent a right pneumonectomy, under a video-assisted thoracic surgery (VATS) approach, as the diffuse small pulmonary arteriovenous malformation involved the whole right lung.

키워드

참고문헌

  1. Gossage JR, Kanj G. Pulmonary arteriovenous malforrnations: a state of the art review. Am J Respir Crit Care Med 1998;158:643-61 https://doi.org/10.1164/ajrccm.158.2.9711041
  2. Vase, P, Holm M, Arendrup H. Pulmonary arterioven ous fistulas in hereditary hemorrhagic telangiectasia. Acta Med Scand 19855218:109-9
  3. Hodgson CH, Burchell HB, Good CA, Claggett OT. Hereditary hemorrhagic telangiectasis and pulmonary arteriovenous fistula. N Engl J Med 1959261:625-36 https://doi.org/10.1056/NEJM195909242611301
  4. Ahn JB, Kim IS, Jung SC, Kim WS, Shin YC, Yoo HK, et al, Pulmonary arteriovenous fistula with he mothorax. Korean J Thorac Cardiovesc Surg 2004; 37:702-6
  5. Cottin V, Hauchu H. Bayle JY, Barthelet M, Revel D, Cordier JF. Pulmonary arteriovenous malformations in patients wi th bereditary berrorrhegic telangiec tasia. Am J Respir Crit Care Med 2004;169:994-1000 https://doi.org/10.1164/rccm.200310-1441OC
  6. Dines DE, Arms RA, Bematz PE, Carnes MR. Pulmonaryarteriovenous fistulas. Mayo Clin Proc 1974;49:460 - 5
  7. White RI Jr, Lynch-Nylan A, Terry P, Buescher PC, Farmlett EJ, Charnas L, et al. Pulmonary arteriovenous malformations: techni ques and long-term out rome of emholotherapy. Radiology 1988;169:163 - 9 https://doi.org/10.1148/radiology.169.1.3420254
  8. Shannon T, Pollak J, White RI. Redisllihution of pulmonary blood flow by embolothempy; a new method for improving oxygenation in patients with diffuse pulmonary arteriovenous malformations [Abstract], Am Rev Respir Dis 1992;145:600A https://doi.org/10.1164/ajrccm/145.3.600
  9. Hepburn J, Dauphinee JA. Successful removal of hemangioma of lung followed by disappearance of polycythemia. Am J Med Sci 1942;204:681-7 https://doi.org/10.1097/00000441-194211000-00007
  10. Wallenhaupt SL, D'Souza V. Combined radiological and surgical management of arteriovenous malformation of the lung. Ann Thorac Surg 1988;45:213-5 https://doi.org/10.1016/S0003-4975(10)62441-1
  11. Ternes RT, Paramsothy P, Endara SA, Werrly JA. Resection of a solitary pulmonary arteriovenous malformation by video-assisted thoracic surgery, J Thorae Cardiovasc Surg 1998;116:878-9 https://doi.org/10.1016/S0022-5223(98)00441-3
  12. Thung KH, Sihoe AD,Wan IY, Lee TW, Wong R, Yim AP. Hemoptysis from an unusual pulmonary arte riovenous malformation. Ann Thorac Surg 2003;76:1730-3 https://doi.org/10.1016/S0003-4975(03)00685-4
  13. Frughnan ME, Lui YW, Wirth JA, Pugash RA, Redelmeier DA, Hyland RH, et al. Diffuse pulmonary arteriovenous malformations: cbarecteristics and prognosis. Chest 2000;117:31-8 https://doi.org/10.1378/chest.117.1.31
  14. Jeong WK, Jeon SC, Choi YW, Park CK, Hong EK, Yoon HJ, et al. Telangiectatic pulmonary arteriovenous malformation. J Tborac Imaging 200318:113-5 https://doi.org/10.1097/00005382-200304000-00013
  15. Jeon YB, Lee JK, Kim JH, Lee DC, Kim DS. Two cases of diffuse type of pulmonary artericvenous fistula. Korean J Med 1986;30: 555-61