A Case of Behcet's Disease with Multiple Cavitary Lung Lesion

다발성 폐공동을 형성한 베체트병 1예

  • Yoon, Se Hee (Department of Internal Medicine, Konyang University College of Medicine) ;
  • Son, Ji Woong (Department of Internal Medicine, Konyang University College of Medicine) ;
  • Joung, Chung Il (Department of Internal Medicine, Konyang University College of Medicine) ;
  • Choi, Eu Gene (Department of Internal Medicine, Konyang University College of Medicine)
  • 윤세희 (건양대학교 의과대학 내과학교실) ;
  • 손지웅 (건양대학교 의과대학 내과학교실) ;
  • 정청일 (건양대학교 의과대학 내과학교실) ;
  • 최유진 (건양대학교 의과대학 내과학교실)
  • Received : 2006.04.18
  • Accepted : 2006.06.20
  • Published : 2006.07.30

Abstract

Behcet's disease is a systemic vasculitis of an unknown etiology involving the arteries and veins of all sizes. There are reports showing that a pulmonary artery aneurysm or thromboembolism and superior vena cava thrombosis are present in 5-10% of patients with Behcet's disease and that lung parenchymal lesions are mainly airway consolidations resulting from hemorrhage or infarction. We encountered a patient with increasing pulmonary cavitary changes and localized aspergilloma. The patient was a 43-year-old man diagnosed with Behcet's disease with a history of recurrent oro-genital ulceration and uveitis, and who was administered methotrexate, colchicines, prednisolone. During the follow up he developed progressive dyspnea upon exertion and finger clubbing. Therefore further evaluations were performed. Chest computed tomography showed more advanced consolidations and cavitations than the previous film with the previously known aspergilloma still observable. An open lung biopsy was carried out to determine the presence of malignant changes, which revealed nonspecific vasculitis. Azathioprine was added resultion in an improvement of symptoms.

저자들은 43세 남자환자에서 반복적인 구강궤양을 가지고 있으며 안증상으로 진단한 베체트병 환자에서 폐동맥 색전증, 폐동맥류, 상대정맥 협착등 다양한 폐혈관 침범과 함께 폐아스페르길루스종을 동반한 다발성 공동 형성을 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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