Clinical and Experimental Pediatrics

The Korean Pediatric Society (대한소아청소년과학회)
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Wilms' tumor with polydipsia, polyuria, hyponatremic hypertension and congestive heart failure : a case report

다음, 다뇨, 저나트륨성 고혈압, 심부전증을 보이는 윌름씨 종양 1례

  • Woo, Chul Hee (Department of Pediatrics, College of Medicine, Korea University) ;
  • Jang, Ji Min (Department of Pediatrics, College of Medicine, Korea University) ;
  • Woo, Chan Wook (Department of Pediatrics, College of Medicine, Korea University) ;
  • Lee, Ki Hyung (Department of Pediatrics, College of Medicine, Korea University) ;
  • Lee, Kwang Chul (Department of Pediatrics, College of Medicine, Korea University)
  • 우철희 (고려대학교 의과대학 소아과교실) ;
  • 장지민 (고려대학교 의과대학 소아과교실) ;
  • 우찬욱 (고려대학교 의과대학 소아과교실) ;
  • 이기형 (고려대학교 의과대학 소아과교실) ;
  • 이광철 (고려대학교 의과대학 소아과교실)
  • Received : 2005.08.12
  • Accepted : 2005.10.04
  • Published : 2006.01.15
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Abstract

A 3-year-old girl presented with polydipsia, polyuria, hyponatremia, hypertension and congestive heart failure. Her polyuria was unresponsive to water restriction and vasopressin challenge tests, and her blood pressure was not effectively controlled by antihypertensive drugs. Radiologic examinations revealed a Wilms' tumor in the right kidney. Her plasma renin activity and aldosterone concentration were greatly increased. After surgical removal of the tumor, the congestive heart failure disappeared. Congestive heart failure due to Wilms' tumor is very rare and we report here on such a case, with a brief review of the literature.

윌름씨 종양은 주로 1-5세에 복부에 생기는 종양으로 약 25% 이상에서 고혈압을 동반하지만 심각한 고혈압에 의하여 심부전을 보이는 경우는 매우 드물다. 저자들은 3세된 여자 아이가 윌름씨 종양으로 인한 고레닌 혈증으로 다음, 다뇨, 저나트륨성 고혈압과 심부전을 보였으나 수술적으로 종양을 제거한 후 증상 호전을 보였기에 문헌 고찰과 함께 보고하는 바이다.

Keywords

References

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