Clinical and Experimental Pediatrics

대한소아청소년과학회 (The Korean Pediatric Society)
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보체 인자 9 결핍을 동반한 수막구균성 수막염 1례

A Case of Meningococcal Meningitis with Complement 9 Deficiency

  • 최선미 (가톨릭대학교 의과대학 소아과학교실) ;
  • 이경일 (가톨릭대학교 의과대학 소아과학교실) ;
  • 이형신 (가톨릭대학교 의과대학 소아과학교실) ;
  • 홍자현 (가톨릭대학교 의과대학 소아과학교실) ;
  • 이미희 (가톨릭대학교 의과대학 소아과학교실) ;
  • 이병철 (가톨릭대학교 의과대학 소아과학교실)
  • Choi, Sun-Mee (Department of Pediatrics, College of Medicine, The Catholic University of Korea) ;
  • Lee, Kyung-Yil (Department of Pediatrics, College of Medicine, The Catholic University of Korea) ;
  • Lee, Hyung-Shin (Department of Pediatrics, College of Medicine, The Catholic University of Korea) ;
  • Hong, Ja-Hyun (Department of Pediatrics, College of Medicine, The Catholic University of Korea) ;
  • Lee, Mi-Hee (Department of Pediatrics, College of Medicine, The Catholic University of Korea) ;
  • Lee, Byung-Cheol (Department of Pediatrics, College of Medicine, The Catholic University of Korea)
  • 투고 : 2004.08.10
  • 심사 : 2004.09.23
  • 발행 : 2005.01.15
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초록

저자들은 12세 여아로 수막구균 수막염에 이환 후 시행한 보체 검사에서 C9 결핍을 확인한 1례를 경험하였다. 수막구균 수막염에 이환된 환아에 대한 보체 검사는 보체 결핍을 갖는 환자와 가족 내 위험이 있는 사람을 찾아내어, 향후 예방접종 등의 예방과 감염 관리에 필요하다.

Meningococcal disease is not rarely associated with abnormalities of the complement system. We experienced a case of C9 deficiency with meningococcal meningitis from a 12-year-old girl. Identification of complement deficiency has implications for management, including family studies, prophylaxis, vaccination, and altered threshold for infection screening and treatment.

키워드

참고문헌

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