Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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Congenital Bronchial Atresia

선천성 기관지 폐쇄증

  • Choi, Yo Won (Department of Diagnostic Radiology, Hanyang University College of Medicine) ;
  • Yoon, Ho Joo (Department of Internal Medicine, Hanyang University College of Medicine) ;
  • Shin, Dong Ho (Department of Internal Medicine, Hanyang University College of Medicine) ;
  • Park, Sung Soo (Department of Internal Medicine, Hanyang University College of Medicine)
  • 최요원 (한양대학교 의과대학 진단방사선과학교실) ;
  • 윤호주 (한양대학교 의과대학 호흡기내과학교실) ;
  • 신동호 (한양대학교 의과대학 호흡기내과학교실) ;
  • 박성수 (한양대학교 의과대학 호흡기내과학교실)
  • Published : 2004.04.30
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Abstract

Congenital bronchial atresia is a rare anomaly, which results from a congenital focal obliteration of a proximal segmental or subsegmental bronchus, with normal development of the distal structures. The short atretic segment leads to the accumulation of mucus within the distal bronchi, forming a bronchocele and air trapping of the alveoli supplied by these bronchi. The diagnostic CT features include the presence of a branching opacity and the bronchocele, which radiate from the hilum and are surrounded by an area of hyperlucency.

선천성 기관지 폐쇄증은 단순촬영에서 폐 결절로 보여 악성 종양으로 오인될 수 있다. 그러나 흉부단순촬영과 특히 전산화단층촬영에서는 늘어난 기관지 내의 점액고착, 구역 과팽창 등이 특징적으로 보여 더 이상의 침습적 검사 없이 선천성 기관지 폐쇄증으로 진단할 수 있다.

Keywords

References

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