흉벽에 발생한 유척삭종(Parachordoma) -1예 보고-

Parachordoma of the Chest Wall -1 case report-

  • 박기성 (대구가톨릭대학교 의과대학 흉부외과학교실)
  • 발행 : 2004.10.01

초록

유척삭종(parachordoma)은 팔, 다리, 가슴에 주로 발생하며 천천히 자라는 저등급 악성 종양으로 알려져 있다. 대표적인 감별진단으로는 척삭종(chordoma), 뼈외 점액양 연골육종(extraskeletal myxoid chondrosarcoma) 등이 있으며, 조직학적 검사와 함께 면역조직화학적 검사가 감별진단에 도움이 된다. 저자는 우측 흉벽에 발생한 유척삭종을 광범위 절제 및 흉벽 재건술 후 16개월 동안 재발없이 추적 관찰한 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Parachordoma is a very rare, slow-growing, and low-grade malignant tumor that occurs in the extremities and trunk. The differential diagnosis includes extraskeletal myxoid chondrosarcoma and chordoma in the histologic finding. Thus, histologic findings with immunohistochemistry may be helpful in distinguishing parachordoma from extraskeletal myxoid chondrosarcoma and chordoma. I report with a brief review of literatures one case of parachordoma of the chest wall which was successfully treated by en-bloc resection and chest wall reconstruction using 2 mm Gore-Tex$^{\circledR}$ soft tissue patch and free from recurrence for 16 months.

키워드

참고문헌

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