Childhood Kidney Diseases
- 제7권1호
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- Pages.96-102
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- 2003
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- 2384-0242(pISSN)
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- 2384-0250(eISSN)
메틸말로닌산혈증에 의한 신생아 고암모니아혈증에서 지속적 정정맥 투석 여과법 시행 1례
A Case of Continuous Venovenous Hemodiafiltration in the Treatment of Neonatal Hyperammonemia Due to Methylmalonic Acidemia
- 장원경 (울산대학교 의과대학 서울아산병원 소아과) ;
- 한혜원 (울산대학교 의과대학 서울아산병원 소아과) ;
- 신영림 (울산대학교 의과대학 서울아산병원 소아과) ;
- 박현경 (울산대학교 의과대학 서울아산병원 소아과) ;
- 김애란 (울산대학교 의과대학 서울아산병원 소아과) ;
-
유한욱
(울산대학교 의과대학 서울아산병원 소아과)
;
-
박영서
(울산대학교 의과대학 서울아산병원 소아과)
- Jhang Won-Kyoung (Department of Pediatrics, Asan Medical Center, University of Ulsan College of Medicine) ;
- Hahn Hye-Won (Department of Pediatrics, Asan Medical Center, University of Ulsan College of Medicine) ;
- Shin Young-Lim (Department of Pediatrics, Asan Medical Center, University of Ulsan College of Medicine) ;
- Park Hyun-Kyung (Department of Pediatrics, Asan Medical Center, University of Ulsan College of Medicine) ;
- Kim Ai-Rhan (Department of Pediatrics, Asan Medical Center, University of Ulsan College of Medicine) ;
-
Yoo Han-Wook
(Department of Pediatrics, Asan Medical Center, University of Ulsan College of Medicine)
;
-
Park Young-Seo
(Department of Pediatrics, Asan Medical Center, University of Ulsan College of Medicine)
- 발행 : 2003.04.01
초록
저자들은 methymalonic acidemia로 진단된 체중 2.4 kg의 생후 5일된 여아에서 지속적 정정맥 투석 여과법(CVVHDF)을 이용하여 혈역학적 불안정 상태나 특별한 후유증 없이 체내 암모니아를 효과적으로 제거하였기에 보고하는 바이다.
Acute hyperammonemia is a medical emergency in the newborn. Efficient, prompt removal of serum ammonia is essential in preventing irreversible brain damage in order to prevent the profound central nervous system dysfunction due to hyperammonia. We report a case of 2.3 kg, 5-day old girl with methylmalonic acidemia who presented with severe hyperammonemia and was successfully treated with continuous venovenous hemodiafiltration(CVVHDF). CVVHDF is an effective and safe method of ammonia removal in the newborn.