Clinical and Experimental Reproductive Medicine

The Korean Society for Reproductive Medicine (대한생식의학회)
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A Case of Mayer-Rokitansky-$K{\ddot{u}}ster$-Hauser Syndrome Accompanying Endometriosis

자궁내막증이 동반된 Mayer-Rokitansky-$K{\ddot{u}}ster$-Hauser 증후군의 수술적 치료경험 1례

  • Park, Jeong-Yeol (Department of Obstetrics and Gynecology, College of Medicine, University of Ulsan, Asan Medical Center) ;
  • Kim, Chung-Hoon (Department of Obstetrics and Gynecology, College of Medicine, University of Ulsan, Asan Medical Center) ;
  • Kang, Cheon-Sik (Department of Obstetrics and Gynecology, College of Medicine, University of Ulsan, Asan Medical Center) ;
  • Lee, Ji-Young (Department of Obstetrics and Gynecology, College of Medicine, University of Ulsan, Asan Medical Center) ;
  • Park, So-Youn (Department of Obstetrics and Gynecology, College of Medicine, University of Ulsan, Asan Medical Center) ;
  • Kim, Sung-Hoon (Department of Obstetrics and Gynecology, College of Medicine, University of Ulsan, Asan Medical Center) ;
  • Chae, Hee-Dong (Department of Obstetrics and Gynecology, College of Medicine, University of Ulsan, Asan Medical Center) ;
  • Kang, Byung-Moon (Department of Obstetrics and Gynecology, College of Medicine, University of Ulsan, Asan Medical Center)
  • 박정열 (울산대학교 의과대학 서울아산병원 산부인과학교실) ;
  • 김정훈 (울산대학교 의과대학 서울아산병원 산부인과학교실) ;
  • 강천식 (울산대학교 의과대학 서울아산병원 산부인과학교실) ;
  • 이지영 (울산대학교 의과대학 서울아산병원 산부인과학교실) ;
  • 박소연 (울산대학교 의과대학 서울아산병원 산부인과학교실) ;
  • 김성훈 (울산대학교 의과대학 서울아산병원 산부인과학교실) ;
  • 채희동 (울산대학교 의과대학 서울아산병원 산부인과학교실) ;
  • 강병문 (울산대학교 의과대학 서울아산병원 산부인과학교실)
  • Published : 2003.06.30
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Abstract

The Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome refers to a condition which presents as normal female secondary sex characteristics, normal external genitalia, congenital absence of the internal vagina, usually a rudimentary uterus in the form of bilateral noncanaliculated muscular buds, and normal tubes and ovaries with normal cytogenetic and endocrine evaluation, frequent association of renal, skeletal and other congenital anomalies. However, rarely, whole uterus or a segment of uterus may be present, but lacking a conduit to the introitus. If a partial endometial cavity is present in a segment of uterus, cyclic abdominal pain may be a complaint and furthermore endometiosis can be developed. Recently, we experienced a case of MRKH syndrome with the segments of uterus accompanying endometriosis in young woman. We present this case with a brief review of literatures.

Keywords

References

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