Surgical Repair of Truncus Arteriosus in an Low-Birth Weight Premature Baby: Right Ventricular Outflow Reconstruction with Valveless Autologous Pericardial Conduit and the Result of 20-Month′s Follow-up

저체중조산아에서 동맥간의 교정 1예: 무판막 자가심낭도관의 이용과 20개월간의 추적결과

  • 성시찬 (부산대학교 의과대학 흉부외과학교실) ;
  • 양승인 (부산대학교 의과대학 흉부외과학교실) ;
  • 이헝두 (부산대학교 의과대학 소아과학교실) ;
  • 김시호 (동아대학교 의과대학 흉부외과학교실) ;
  • 우종수 (동아대학교 의과대학 흉부외과학교실) ;
  • 이영석 (동아대학교 의과대학 소아과학교실)
  • Published : 2003.10.01

Abstract

It is known that low birth weight is a risk factor for poor outcome in cardiac surgery for many cardiac defects. Truncus arteriosus is a rare congenital anomaly that has an unfavorable natural course. We report a successful surgical correction of truncus arteriosus in an 13-day-old premature infant with body weight of 1.5 kg and gestational age of 32 weeks. We used autologous untreated pericardial conduit without valve in right ventricular outflow reconstruction. The patients remains in good condition with normal body weight (50 percentile) and wide right ventricular outflow tract 20 months after the operation.

저체중 출생아는 선천성 심장 기형의 수술 시 위험요소가 많은 것으로 알려져 있으며, 동맥간은 매우 불량한 자연경과를 갖고 있는 비교적 희귀한 심장기형이다. 제태기간 32주의 생후 13일된, 수술 당시체중 1.5 kg이었던 저체중 조산아에서 우심실 유출로 재건에 무판막 자가심낭도관을 사용하여 동맥간을 성공적으로 완전교정하고 술 후 약 20개월간의 양호한 추적결과를 경험하였기에 보고하는 바이다.

Keywords

References

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