Tuberculosis and Respiratory Diseases
- Volume 52 Issue 3
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- Pages.278-282
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- 2002
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- 1738-3536(pISSN)
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- 2005-6184(eISSN)
Idiopathic Fibrosing Mediastinitis Causing Extensive Fibrotic Veno-occlusion with Minimal Mediastinal Involvement
광범위한 섬유성 정맥 폐쇄를 동반한 특발성 섬유화성 종격동염 1예
- Kim, Je-Hyeong (Department of Internal Medicine, College of Medicine, Korea University) ;
- Hur, Gyu-Young (Department of Internal Medicine, College of Medicine, Korea University) ;
- Lee, Seung-Heon (Department of Internal Medicine, College of Medicine, Korea University) ;
- Lee, Sang-Yeub (Department of Internal Medicine, College of Medicine, Korea University) ;
- Park, Sang-Myun (Department of Pathology, College of Medicine, Korea University) ;
- Shin, Chol (Department of Internal Medicine, College of Medicine, Korea University) ;
- Shim, Jae-Jeong (Department of Internal Medicine, College of Medicine, Korea University) ;
- In, Kwang-Ho (Department of Internal Medicine, College of Medicine, Korea University) ;
- Kim, Han-Kyeom (Department of Pathology, College of Medicine, Wonkwang University) ;
- Kang, Kyung-Ho (Department of Internal Medicine, College of Medicine, Korea University) ;
- Yoo, Se-Hwa (Department of Internal Medicine, College of Medicine, Korea University)
- 김제형 (고려대학교 의과대학 내과학교실) ;
- 허규영 (고려대학교 의과대학 내과학교실) ;
- 이승헌 (고려대학교 의과대학 내과학교실) ;
- 이상엽 (고려대학교 의과대학 내과학교실) ;
- 박상면 (원광대학교 의과대학 내과학교실) ;
- 신철 (고려대학교 의과대학 내과학교실) ;
- 심재정 (고려대학교 의과대학 내과학교실) ;
- 인광호 (고려대학교 의과대학 내과학교실) ;
- 김한겸 (고려대학교 의과대학 병리학교실) ;
- 강경호 (고려대학교 의과대학 내과학교실) ;
- 유세화 (고려대학교 의과대학 내과학교실)
- Published : 2002.03.30
Abstract
A 68-year-old woman was admitted after suffering facial edema with neck vein engorgement for approximately 2 months. A chest X-ray showed a mild widening of the superior mediastinum and a luminal obliteration of the superior vena cava(SVC) was noted on a computed tomograph. Venography showed that both subclavian veins were obstructed at the level of the proximal clavicle with a nonvisualization of the SVC. The SVC, both the innominate and the left internal jugular veins were completely obstructed with extensive cord-like fibrotic changes despite the absence of mediastinal involvement. The microscopic features showed a chronic granulomatous inflammation with a fibrosis minimally invading the mediastinal fat, which is consistent with fibrosing mediastinitis.
특발성 섬유화성 종격동염은 일반적으로 일차적인 종격동의 섬유화 및 석회화가 종격동 기관을 침범하거나 압박함으로써 상대정맥증후군 등의 임상양상을 나타내는 질환이다. 그러나 저자등은 종격동의 침범은 아주 경미하면서도 광범위하고 심한 종격동 혈관의 섬유성 폐쇄를 동반한 특발성 섬유화성 종격동염 1예를 경험하였기에 보고하는 바이다.