Tetralogy of Fallot with Pulmonary Arteriovenous Fistula -A Case Report-

폐동정맥루를 동반한 팔로사징환자의 치험 -1례보고-

  • 김상익 (가천의과대학부속길병원 흉부외과) ;
  • 박국양 (가천의과대학부속길병원 흉부외과) ;
  • 박철현 (가천의과대학부속길병원 흉부외과) ;
  • 김정철 (가천의과대학부속길병원 흉부외과) ;
  • 현성열 (가천의과대학부속길병원 흉부외과) ;
  • 이재웅 (가천의과대학부속길병원 흉부외과) ;
  • 이현우 (가천의과대학부속길병원 흉부외과) ;
  • 이성재 (가천의과대학부속길병원 심장소아과) ;
  • 김종호 (가천의과대학부속길병원 핵의학과)
  • Published : 2000.03.01

Abstract

Pulmonary arteriovenous fistula can occur in a variety of clinical situations including liver diseases, infections, metastatic carcinomas, systemic disorders, and after the palliation of congenital heart diseases. A 72-day-old male infant with Tetralogy of Fallot and pulmonary atresia underwent surgical correction without difficulty. However, ventilator weaning in the ICU failed initially because of an unexplained postoperative hypoxemia(FiO2: 0.8, PaO2: 40 mmHg, SaO2: 80∼90%). Postoperative follow-up lung perfusin scan at postoperative 15 days showed right-to-left shunt(33.6%) and ventilator weaning was performed on the 20th day after the operation (FiO2: 0.4, PaO2, 50mmHg, SaO2: 86.9%). Arterial oxygen saturation under room air was 80∼85% at 7 months postoperatively. One and half year follow-up lung perfusion scan showed decreased amount of right-to-left shunt (11.2%). We report a case with a review of the literatures.

Keywords

References

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