One Stage Correction of the Pectus Excavatum with Marfan Syndrome

Marfan증후군의 수술 교정 1례

  • Lee, Seung-Yeol (Dept.of Thoracic and Cardiovascular Surgery, College of Medicine, Korea University) ;
  • Nam, Yeong-Su (Dept.of Thoracic Surgery, Medical School, Hanyang University) ;
  • Kim, Hyeong-Muk (Dept.of Thoracic and Cardiovascular Surgery, College of Medicine, Korea University)
  • 이승열 (고려대학교 의과대학 흉부외과) ;
  • 남영수 (한양대학교 의과대학 흉부외과) ;
  • 김형묵 (고려대학교 의과대학 흉부외과)
  • Published : 1995.01.01

Abstract

Pectus excavatum occasionally occurs in patients who have underlying cardiac disease, especially Marfan syndrome. This report describes a patient with pectus excavatum who had ascending aortic aneurysm with aortic regurgitation and anterior leaflet prolapse of mitral valve. This patient underwent replacement of aortic valve and ascending aorta with 25 mm SJM valved conduit graft[Bentall operation with Cabrol shunt , and mitral valve replacement with SJM 31 mm, the pectus excavatum was corrected at the time of completion of the intracardiac operation with the modified sternal turnover. This procedure offered excellent operative exposure for the inracardiac operation with prevention of low cardiac output after operation due to depressed sternum and maintained chest wall stability resulting good cosmetic chest wall appearance. This patient recovered and discharged in good postoperative result with minimal temporary peroneal nerve palsy in his left leg.

Keywords

References

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