A Case Report of Mediastinal Leiomyosarcoma

종격동내 평활근육종 1예

  • Lee, Won-Yeon (Department of Internal Medicine, Wonju College of Medicine, Yonsei University) ;
  • Ahn, Kang-Hyun (Department of Internal Medicine, Wonju College of Medicine, Yonsei University) ;
  • Jung, Soon-Hee (Department of Pathology, Wonju College of Medicine, Yonsei University) ;
  • Koh, Jae-Hyang (Department of Pathology, Wonju College of Medicine, Yonsei University) ;
  • Yoo, Byung-Soo (Department of Internal Medicine, Wonju College of Medicine, Yonsei University) ;
  • Yong, Suk-Joong (Department of Internal Medicine, Wonju College of Medicine, Yonsei University) ;
  • Shin, Kye-Chul (Department of Internal Medicine, Wonju College of Medicine, Yonsei University)
  • 이원연 (연세대학교 원주의과대학 내과학교실) ;
  • 안강현 (연세대학교 원주의과대학 내과학교실) ;
  • 정순희 (연세대학교 원주의과대학 병리학교실) ;
  • 고재향 (연세대학교 원주의과대학 병리학교실) ;
  • 유병수 (연세대학교 원주의과대학 내과학교실) ;
  • 용석중 (연세대학교 원주의과대학 내과학교실) ;
  • 신계철 (연세대학교 원주의과대학 내과학교실)
  • Published : 1994.12.31

Abstract

The leiomyosarcoma is uncommon tumor that consists of 10% of all sarcoma incidence and commonly arise from retroperitoneum or mesentery. But leiomyosarcoma arose from mediastinum is very rare and only incidental case report is present. Mediastinal leiomyosarcoma may originate from superior vena cava, pulmonary artery, small vessels of alveoli, esophagus and cardiac muscle. Common symptoms that are related with leiomyosarcoma of mediastinum are cough and dyspnea but dysphagia, chest pain and hemoptysis can be produced. Although long term survival after complete resection of tumor was reported in localized disease, there was no effective therapy that prolong the survival in patients who had disseminated disease or huge tumor mass. We report the case of posterior mediastinal leiomyosarcoma confirmed by aspiration cytology and immunohistochemical staining, along with a review of literature.

저자등은 종격동에서 늑막삼출액과 함께 종물이 있는 소견을 보였던 환자에서 세포진검사 및 면역화학적 검사를 통하여 평활근육종으로 진단된 1예를 경험하였기에 문헌고찰과 함께 이를 보고하는 바이다.

Keywords