• Title/Summary/Keyword: primary congenital

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기관 식도루가 없는 선천성 식도 폐쇄 (Suryical Treatment of Congenital Esophayeal Atresia without Tracheoesophageal Fistula -A Case Report of Staged Operation-)

  • 김영대
    • Journal of Chest Surgery
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    • 제27권12호
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    • pp.1052-1055
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    • 1994
  • Congenital esophageal atresia without tracheoesophageal fistula which called isolated esophageal atresia is a very rare entity and the neonate classified as category C by Waterston`s classification has high mortality rate. We experienced a case of isolated esophageal atresia. This patient was a male with 1,750gm in body weight and had been suffered from bilateral pneumonia. The patient was managed with staged operation. Feeding gastrostomy was made as the first intervention and delayed primary anastomosis was performed 3 months later. The postoperative course was uneventful and he was discharged on the 22nd postoperative day.

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선천성 낭포성 유선종 기형 (Congenital Cystic Adenomatoid Malformation(CCAM))

  • 김수원
    • Journal of Chest Surgery
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    • 제21권6호
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    • pp.1084-1094
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    • 1988
  • Conservative management of 3 iatrogenic perforations of intrathoracic esophagus was reviewed. The primary disorders were achalasia in 2 patients and congenital tracheoesophageal fistula in 1 patient. Perforation occurred after treatment of the primary disorders in the distal esophagus in 2 patients and mid-thoracic esophagus in 1 patient. All the perforations appeared late after the previous treatments and the inflammation spread to mediastinum and pleural cavity in all the 3 patients. Conservative management of esophageal perforation was carried out with intraluminal drainage from the perforated site of esophagus[insertion of Levin`s tube and continuous suction], pleural drainage and feeding of liquid diet through gastrostomy tube with Fowler`s position. The patients revealed spontaneous closure of perforated sites about 3 to 4 weeks after this conservative management without open thoracotomy. This result suggests that this conservative management may be accepted as therapeutic method in the thoracic esophageal perforations regardless of cause and time of the perforation.

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우심증에 동반된 선천성 심장질환의 치험 2례 (Two Cases Reports of Dextrocardia with Congenital Heart Disease)

  • 김준우;김원곤;유세영
    • Journal of Chest Surgery
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    • 제28권7호
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    • pp.698-703
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    • 1995
  • Dextrocardia means right-sided position of the heart in the chest irrespective of the cause. For the absolute diagnosis of the dextrocardia, the segmental analysis of heart is necessary. Once the segmental analysis of the dextrocardia is made, it is often relatively easy to identify the presence of any associated defects based on conventional methods including physical examination, EKG, echocardiography, and angiocardiography. Two cases of dextrocardia with congenital heart disease were treated surgically.A eleven - months old boy was operated under diagnosis of ASD, VSD, and bilateral SVC with mirror - image dextrocardia {I,L,I} by primary closure of ASD and VSD.A twenty-four months old girl was operated under diagnosis of ASD, VSD, and PS with corrected TGA {I,D,D} by primary closure of ASD, VSD and dilatation of pulmonary stenosis. Both of them were discharged healthily after operation.

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Focal Spinal Nondisjunction in Primary Neurulation : Limited Dorsal Myeloschisis and Congenital Spinal Dermal Sinus Tract

  • Wong, Sui-To;Pang, Dachling
    • Journal of Korean Neurosurgical Society
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    • 제64권2호
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    • pp.151-188
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    • 2021
  • Spinal dysraphic lesions due to focal nondisjunction in primary neurulation are commonly encountered in paediatric neurosurgery, but the "fog-of-war" on these conditions was only gradually dispersed in the past 10 years by the works of the groups led by the senior author and Prof. Kyu-Chang Wang. It is now clear that limited dorsal myeloschisis and congenital spinal dermal sinus tract are conditions at the two ends of a spectrum; and mixed lesions of them with various configurations exist. This review article summarizes the current understanding of these conditions' embryogenetic mechanisms, pathological anatomy and clinical manifestations, and their management strategy and surgical techniques.

개심술후 재수술에 대한 임상적 고찰 (Reoperation after Open Heart Surgery -Clinical analysis of 27 cases-)

  • 서의수
    • Journal of Chest Surgery
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    • 제22권1호
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    • pp.50-58
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    • 1989
  • The emergence and expansion of cardiac surgery over the past decade has resulted in an increasing number of patients undergoing cardiac operations but many kinds of heart surgery was realized only palliative, resulting in increasing numbers of secondary cardiac procedures. From 1978 to 1988, 10 cases of various congenital heart diseases and 17 cases of acquired heart diseases were reoperated at Hanyang University Hospital. The leading indication of second operation was residual shunt or valvular malfunction due to technical failure in congenital heart disease and primary valve failure, endocarditis, paravalvular leakage were for acquired heart disease. The mortality of reoperation was 0% for congenital heart disease and 11.7%[2 death among the 17 patients] for acquired heart disease. The leading causes of death were myocardial failure, sepsis with endocarditis, acute renal failure and congestive heart failure.

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부주상골을 동반한 이분 내측 설상골: 증례 보고 (Bipartite Medial Cuneiform Combined with Accessory Navicular: A Case Report)

  • 이태훈;남일현;문기혁;이영현;안길영;이영훈
    • 대한족부족관절학회지
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    • 제19권1호
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    • pp.32-34
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    • 2015
  • Accessory navicular is a congenital anomaly appearing in the secondary ossification center on the tuberosity of the navicular that may cause flatfoot. Bipartite medial cuneiform is another rare congenital anomaly occurring as two primary ossification centers in the medial cuneiform. The authors report a rare case of symptomatic bilateral accessory navicular with bipartite medial cuneiform and flatfoot deformity in a 19-year-old man with a review of the literature.

선천성 식도폐쇄증 4례 보고 (Congenital Esophageal Atresia: Report of Four Cases)

  • 노준량
    • Journal of Chest Surgery
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    • 제5권2호
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    • pp.153-158
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    • 1972
  • The esophageal atresia with tracheoesophageal fistula occurs approximately once in 3, 000 live births. In Korea, about 20 cases were reported with five successful surgical corrections. The atresia characteristically occurs at the level of, or just cephalad to, the carina and is associated with a tracheoesophageal fistula. In about 90% of the cases, the upper esophagus ends in a blind pouch, and the lower esophageal segment communicates with the trachea through the membranous posterior wall just above the carina. Many of the Infants with esophageal atresia have other congenital anomalies. The most common of these are congenital cardiac anomalies, imperforate anus, genitourinary malformations, and intestinal atresia. Recently we experienced four cases of esophageal atresia, of which three were Gross type C and one was type A. Two of them were treated by primary repair, and one [type A] was taken cervical esophagostomy and gastrostomy. The another was refused surgery.

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완전 흉골열 - 1례 보고 - (Complete Sternal Cleft)

  • 신제균
    • Journal of Chest Surgery
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    • 제32권10호
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    • pp.966-969
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    • 1999
  • Congenital defects of the sternum are rare development anomalies. They result form the failure of the lateral sternal bars to fuse. This malformation may be associated with other ventral midline fusion defects and ectopia cordis. A complete sternal cleft is the rarest form and less than 10 cases have been reported in the medical literature. Here were report a 3-day-old boy with complete sternal cleft without other malformations, who underwent primary surgical repair. Surgical correction of complete sternal cleft should be performed in neonatal period whether the infant if symptomatic or not because it is usually simple, able to achieve good result and primary repair is usually feasible at this period.

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X선에 의한 유합치와 계승치에 관한 통계학적 고찰 (The Statistical Study on Primary Fused Teeth and The Corresponding Permanent Teeth by Orthopantomograph)

  • 박병진;조사현;우원섭
    • 대한치과의사협회지
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    • 제11권5호
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    • pp.313-316
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    • 1973
  • 970 children visited attached hospital, S.N.U, were taken orthopantomograph. Of those children, there were 14 patients who have primary fused teeth. The author observed those cases and got following results. 1) Incidence of primary fused teeth was higher in female. 2) In the order of frequency, fused teeth of mandibular right primary lateral incisor and canine were 9 and that of mandibular left primary lateral incisor and canine were 4, and there was only one case in maxillary. 3) 13 cases showed the congenital absence of lateral incisor of the corresponding permanent teeth. 4) Incidence of fused teeth was 1.44%.

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간질(癎疾)의 원인(原因)에 대한 동서의학적(東西醫學的) 고찰(考察) (The investigation into the cause of epilepsy between east and west medicine)

  • 박지은;권정남;김영균
    • 대한한방내과학회지
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    • 제20권1호
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    • pp.33-47
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    • 1999
  • Through a literal study upon the cause of epilepsy between east and west medicine, next conclusion have been abtained. 1. The cause epilepsy in the east medicine, congenital embryo disease is due to insufficiency of heart(心虛) or deficiency of heart energy(心氣虛), secondary cause is wind -evil(風), frightness(驚), phlegm(痰), fire(火) 2. The cause epilepsy in the west medicine is divided congenital disease and secondary cause, one is excessive discharge of electricity of the brain have on a central nerve, a digestive organ, a respiratory organ, hamatogenous functions, the other is hereditary it and pathological it. 3. The epilepsy is concerned about the abnormality in five viscera, liver, spleen, heart. 4. In comparison east and west medicine of epilepsy is native factor, or innate primary cause is added to outer cause of wind-evil(風), cold-evil(寒), summer-heat(署), wetness(濕), and inner cause of frightness-terror(驚-恐), seven modes of emotions(七情) and the epilepsy is occurred phlegm(痰), fire(火). It similar that the epilepsy is occurred to structural and functional obstacle in western hereditary and primary cause.

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