• Journal of the korean academy of Pediatric Dentistry
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• v.36 no.1
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• pp.150-156
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• 2009

Objectives : The conventional removable appliance, composed of wires and acrylic resin, had unaesthetic results and poor retention. The flexible denture, as an alternative, presents improved aesthetics with the thin and strong resin retentive area. In addition, it also enhances patients' sensory function as a result of decreased volume of denture base. The flexibility of the flexible denture reduces the possibility of fracture and distributes the masticatory forces transmitted to the abutments and residual bone tissue. This report describes a 10-year-old girl and a 6-year-old boy with oligodontia treated with the flexible dentures as an alternative to conventional removable appliances. Methods : Impression was taken using alginate material and sent to a laboratory with the bite for fabrication of the flexible denture. Prior to try-in, the flexible denture was immersed in water at $90^{\circ}C$ for one minute and cooled. Impinging area of the denture was checked by $Fit-Checker^{(R)}$ and removed and the denture was delivered to the patient. Results : Both patients were satisfied with the flexible dentures, which presented improved retention and aesthetics. Conclusion : For patients with oligodontia, flexible dentures can be considered as a treatment of choice, which may replace the conventional denture.

• Journal of the korean academy of Pediatric Dentistry
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• v.43 no.3
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• pp.299-305
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• 2016

The aim of this study was to identify the causative genetic mutation in a family with non-syndromic oligodontia. The 7-year-old female proband and her mother underwent oral examination, panoramic radiographs were obtained and blood samples were collected. All exons of the PAX9 gene were amplified by polymerase chain reaction and sequenced. The sequencing results were compared with the standard human gene sequence. The proband lacked 11 permanent teeth, and her mother lacked 19 permanent teeth. No other birth defects were observed. As a result of gene analysis, there was a novel heterozygous nonsense mutation (c.184G>T, $p.Glu62^*$) in exon 2 in both affected subjects. It is suspected that the nonsense mutation leads premature termination of translation, yields a truncated protein 280 amino acids shorter than the wild-type protein. These defects include parts of the paired box domain, a DNA-binding site that plays an essential role in protein function. Otherwise, more likely the mutant transcript would be degraded by nonsense-mediated decay system, resulting haploinsufficiency to cause oligodontia in this family.

• 대한치과보철학회:학술대회논문집
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• 1999.04a
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• pp.98.1-98.1
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• 1999

• Journal of the korean academy of Pediatric Dentistry
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• v.7 no.1
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• pp.85-93
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• 1980

This study was undertaken in order to observe the prevalence of congenital dental anomalies especially that of oligodontia and supernumerary teeth in 1024 children at age from 4 to 14 years, through history taking, oral examinations, roentgenographic observations of subjects, and statistic analysis was made. The following results were obtained: 1. The prevalence of oligodontia in 1024 children was $6.45{\pm}.8$ percent with a total of 122 teeth absent in sixty-six subjects, excluding 3rd molars, and most of children (86.4%) who have congenitally missing teeth showed abscence of one or two teeth individually. 2. The teeth most frequently absent were the mandibular second premolar, maxillary second premolar, maxillary lateral incisor, mandibular central incisor, and mandibular lateral incisor in order. 3. There was no statistically significant difference found in tooth abscence in the following comparisons; .Male vs Female .Bilateral vs Unilateral .Maxilla vs Mandible .Right vs Left 4. The prevalence of supernumerary teeth in 1024 children was $4.79{\pm}.67$ percent with a total of 59 supernumerary teeth in forty-nine subjects, all of children who have supernumerary teeth showed one or two supernumerary teeth individually. 5. Statistically significant difference was found in supernumerary teeth in the comparison of male vs female, and they were more frequent in male.

• Journal of Oral Medicine and Pain
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• v.31 no.2
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• pp.121-126
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• 2006

Hypohidrotic ectodermal dysplasia refers to a group of disorders with the following common features : thin, sparse or absent hair, missing or peg-shaped teeth and inability to sweat adequately. Both the primary and secondary dentition are affected. Teeth may be absent (anodontia) or reduced in number (oligodontia) and abnormally shaped. In case, A 5-year-old man presented with hypohidrosis and dry skin. He had no teeth in mouth. We report a case of hypohidrotic ectodermal dysplasia with anodontia.

• Journal of the korean academy of Pediatric Dentistry
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• v.26 no.4
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• pp.636-643
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• 1999

Ectodermal dysplasia is a genetic birth defect in which at least abnormally develop two structures derived from the ectoderm. It is usually inherited in autosomal dominant or autosomal recessive pattern. Oral manifestations are oligodontia, anodontia, dysmorphic teeth(conical shape), decreased occlusal vertical dimension and alveolar bone. Extraoral signs may include decreased or absent sweat glands, sparse and fine hair, saddle nose, hearing loss and decreased production of body fluids including saliva. Most affected children require extensive dental treatment to restore their appearance and help the development of a positive self image. The patient's overclosed profile was due to a decreased vertical dimension. The use of overdenture is to preserve erupted teeth, to accomodate the newly constructed occlusal plane, to improve retention and stability of denture and to maintain the remaining alveolar bone. The restoration of vertical dimension improved the child's speech, swallowing, and eating. Growth continue until the age of approximately 18. As child grows, replacement dentures will have to be fabricated primarily to accomodate increasing vertical dimension and changing dentition. Implants may be indicated later if the alveolar bone is adequate. Periodic recall visits are advised, to monitor the dentures during periods of growth and development, and eruption of the permanent teeth.

• Journal of the korean academy of Pediatric Dentistry
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• v.33 no.1
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• pp.122-130
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• 2006

Congenital Missing Teeth(hypodontia, oligodontia) is the developmental absence of one or more teeth. It has been reported as being the most common anomaly of dental development in human, relatively common in the permanent dentition. In a recent review, Vastardis has quoted incidence ranges of $1.6%{\sim}9.6%$ in the permanent dentition. Brook has quoted a prevalence of $3.5%{\sim}6.5%$ in most populations, with severe hypodontia, defined as the absence of six or more teeth, having a prevalence of $0.3{\sim}0.4%$. The most commonly affected teeth are third molars, followed by maxillary lateral incisor, and second premolars. The etiology is unknown, several hypotheses include trauma, nutritional deficiency, infection, metabolic abnormalities, systemic disease and genetic influence. The multiple congenital missing is commonly associated with specific syndrome or severe systemic abnormalities such as cleft lip & palate and Down's syndrome. These cases present that children have multiple congenital missing teeth in the permanent dentition, without any systemic disease. Management of this condition must be considered orthodontic and prosthodontic treatment comprehensively. In these cases, children were treated by space maintainer or orthodontic appliance and follow-up checked.

• Journal of the korean academy of Pediatric Dentistry
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• v.11 no.1
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• pp.255-259
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• 1984

Ectodermal dysplasia is a rare hereditary abnormality of which the outstanding characteristics are hypodontia, hypohidrosis and hypotricosis. Patient afflicted with this malformation shows a typical face resembling that of congenital-syphilis. Dental abnormality (delayed eruption, oligodontia) becomes apparent in this child and causes the parents to bring him to the dentist. Prosthetic appliances are usually indicated and he must be adjusted or be remade as the child matures.

• The Journal of Korean Academy of Prosthodontics
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• v.29 no.1
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• pp.249-254
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• 1991

Two male patients of hereditary ectodermal dysplasia with oligodontia aged 12years and 10years 6months were recalled after 6 years and treated by reconstructing overdentures according to the growth. Patients were improved functionally and cosmetically. Periodic recall is reguired and denture should be reconstructed according ato their growth.

• The Journal of the Korean dental association
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• v.22 no.4 s.179
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• pp.329-332
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• 1984

The author observed a patient of ectodermal dysplasia with oligodontia. The treatments were done as follows: Vital pulpotomy and restorative treatment were done as usual method. Removable type space maintainer was set on the area of primary teeth removed. Follow-up checking were required for the observation of growth and development of the permanent teeth and the jaw.