• 제목/요약/키워드: malformation

검색결과 820건 처리시간 0.022초

Chiari 1.5 Malformation : An Advanced Form of Chiari I Malformation

  • Kim, In-Kyeong;Wang, Kyu-Chang;Kim, In-One;Cho, Byung-Kyu
    • Journal of Korean Neurosurgical Society
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    • 제48권4호
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    • pp.375-379
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    • 2010
  • The Chiari 1.5 malformation is defined as a tonsillar hemiation within a Chiari I malformation with additional caudal descent of the brainstem through the foramen magnum. We describe a patient with Chiari I malformation who evolved to Chiari 1.5 malformation during longitudinal follow-up. A 15-year-old girl presented with neck pain during exercise for two years. She had been diagnosed with Chiari I malformation with mild hydrocephalus after minor cervical trauma at the age of six years. At that time, she was asymptomatic. After she complained of aggravated neck pain, neuroimaging (nine years after first imaging) revealed caudal descent of the brainstem and syringomyelia in addition to progression of tonsillar hemiation. Posterior fossa decompressive surgery resulted in complete resolution of neck pain. Based on neuroimaging and operative findings, she was diagnosed as Chiari 1.5 malformation. Neuroimaging performed seven months after surgery showed an increased anterior-posterior diameter of the medulla oblongata and markedly decreased syringomyelia. This case demonstrates progressive developmental process of the Chiari 1.5 malformation as an advanced form of the Chiari I malformation.

코일 색전술로 치료된 다발성 폐동정맥기형 1 예 (A Case of Multiple Pulmonary Arteriovenous Malformation Treated with Coil Embolization)

  • 안혁수;이흥범;이용철;이양근
    • Tuberculosis and Respiratory Diseases
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    • 제45권4호
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    • pp.896-901
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    • 1998
  • Pulmonary arteriovenous malformation(PAVM) is an uncommon congenital anomaly. As pulmonary arteriovenous malformation is a direct communication between the branches of pulmonary artery and vein which originated from the malformation of capillary development, major disturbances in gas exchange can result. This malformation results in the several symptoms such as dyspnea, hemopyssis, cyanosis, and severe neurologic complaints. However, the most of patients are usually asymptomatic. Selective pulmonary angiography is well known the helpful diagnostic method. Recently, therapeutic embolization has been advocated as the treatment of choice for pulmonary arteriovenous malformations. We report a case of multiple pulmonary arteriovenous malformation, which was detected on the simple chest X-ray and successfully treated with coil embolization in a 19-year-old asymptomatic woman.

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Acquired Chiari Malformation

  • Song, Sang-Woo;Chung, Chun-Kee
    • Journal of Korean Neurosurgical Society
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    • 제40권1호
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    • pp.38-39
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    • 2006
  • Perioperative lumbar drainage of cerebrospinal fluid is commonly used in neurosurgical practice. However, the relationship between lumbar drainage and acquired Chiari malformation is not well established. The authors present an unusual case of paraplegia as a result of acquired Chiari malformation after lumbar drainage. Acquired Chiari malformation can induce compression of cervicomedullary junction and syrinx formation. Foramen magnum decompression is recommended for the solution of such problems.

선천성 낭포성 선종양 기형 -1례 보고- (Congenital Cystic Adenomatoid Malformation)

  • 장기경
    • Journal of Chest Surgery
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    • 제28권7호
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    • pp.726-730
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    • 1995
  • Congenital cystic adenomatoid malformation[CCAM of the lung is extremely rare. We have experienced an unusual case of congenital cystic adenomatoid malformation. The patient was 20-year-old male and had chest pain for 10 days. On simple chest x-ray and Thoracic CT scan, there was a large cystic mass surrounded with multiloculated round cysts with air fluid level on the right lower lobe of a lung. Right lower lobectomy was performed and the pathologic result was congenital cystic adenomatoid malformation.

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족저 내측부의 동정맥 기형: 증례 보고 (Arteriovenous Malformation on the Medial Plantar Area of the Foot: A Case Report)

  • 하대호;권정남;김유미;이준형
    • 대한족부족관절학회지
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    • 제20권4호
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    • pp.187-191
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    • 2016
  • Arteriovenous malformation (A-V malformation) is defined as an abnormal connection between arteries and veins that lead to A-V shunting with an intervening network of vessels. A-V malformation is a rare condition, and spontaneous regression is also rare. A-V malformation becomes symptomatic when the surrounding tissue and osseous structures are negatively affected. A-V malformation has a high recurrence rate and is relatively hard to treat. In this case, a huge mass with pulsatile and bruit on the medial plantar area were observed. With the diagnosis of A-V malformation in accordance with the results from ultrasonography, magnetic resonance imaging and computed tomography angiography, and mass excision with feeding vessel ligation through plantar midfoot approach was completed successfully.

안면부 모세혈관기형에 따른 광범위 안면부 결손의 유리피판술을 이용한 치험례 (Case of Surgical Treatment with Free Flap on Large Size Facial Capillary Malformation)

  • 김도훈;변재경;문구현;방사익;오갑성;임소영
    • Archives of Reconstructive Microsurgery
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    • 제20권1호
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    • pp.60-63
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    • 2011
  • Capillary malformation is common vascular malformation. In case of facial capillary malformation, patients' cosmetic and functional deficits are quite significant. The standard treatment which has been applied so far for capillary malformation is pulsed dye laser with 585nm. But in case of advanced capillary malformation, surgical interventions are inevitable. The problem of large size facial capillary malformation is how to cover the remnant defect, which occurs after resection. In this case, authors have experienced surgical treatment of large size facial capillary malformation and covered the large facial defect with free thoracodorsal artery perforator flap. The flap was thick, so facial asymmetry remained after the first surgery. But with the secondary procedure, authors have made more symmetric figures. The patient was satisfied with the result. Using free flap to replace the defect after resection due to capillary malformation is useful for these kinds of cases.

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Intraneural Venous Malformations of the Median Nerve

  • Porto, Sara Alicia Gonzalez;Rodriguez, Alba Gonzalez;Miguez, Jose Midon
    • Archives of Plastic Surgery
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    • 제43권4호
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    • pp.371-373
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    • 2016
  • Venous malformations arising from the peripheral nerve are a rare type of vascular malformation. We present the first case of an intraneural venous malformation of the median nerve to be reported in a child and review the previous two cases of median nerve compression due to a venous malformation that have been reported. These cases presented with painless masses in the volar aspect of the wrist or with symptoms suggestive of carpal tunnel syndrome. Clinical suspicion should lead to the use of Doppler ultrasonography as the first-line diagnostic tool. Magnetic resonance imaging and histopathology can confirm the diagnosis, as phleboliths are pathognomonic of venous malformations. Surgical treatment appears to be the only modality capable of successfully controlling the growth of an intraneural malformation. Sclerotherapy and radiotherapy have never been used to treat this type of malformation.

이상와에 발생한 정맥 기형에 대한 에탄올 경화치료 1례 (A Case of Venous Malformation of the Pyriform Sinus Treated with Ethanol Sclerotherapy)

  • 양연준;강민수;김상협;문정환
    • 대한후두음성언어의학회지
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    • 제28권2호
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    • pp.135-137
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    • 2017
  • We describe a case of venous malformation of pyriform sinus in 63 year-old patient, discovered incidentally. Venous malformation are the most common vascular malformations to arise in the head and neck. However venous malformation of the hypopharynx in the adult papulation are rare. The author performed successfully ethanol sclerotherapy for venous malformation of pyriform sinus, so we present the case with a review of the related literatures.

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