• 제목/요약/키워드: Willams syndrome

검색결과 3건 처리시간 0.018초

선천성 대동맥 판막 이상과 무명동맥 협착이 동반된 미만성 대동맥 판막상부 협착증 치험 1례 (Diffuse Supravalvar Aortic Stenosis Associated with Congenital Anomaly of the Aortic Valve(Williams Syndrome) -1 case report-)

  • 김수철;전순호
    • Journal of Chest Surgery
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    • 제33권9호
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    • pp.748-751
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    • 2000
  • The diffuse form of supravalvar aortic stenosis represents a surgical challenge when the ascending aorta, aortic arch, proximal descending thoracic aorta and arch arteries are involved. It can be treated by a variety of surgical approaches. We report a case of severe diffuse supravalvar aortic stenosis combined with an aortic valve anomaly and occlusion of the right coronary artery ostium in a 14-year-old boy with Williams syndrome. We enlarged the aortic root(Nick's procedure), ascending aorta, aortic arch, proximal descending thoracic aorta, and innominate artery with patches and replaced aortic valve with 19 mm St. Jude valve. Deep hypothermic circulatory arrest and retrograde cerebral perfusion were used during repair of the arch and arch artery.

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Williams Syndrome 환자에서의 scissor bite correction: 증례보고 (SCISSOR BITE CORRECTION IN PATIENTS WITH WILLAMS SYNDROME: A CASE REPORT)

  • 지은혜;최형준;김성오;손흥규;이제호
    • 대한장애인치과학회지
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    • 제7권1호
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    • pp.21-24
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    • 2011
  • 11세 여환이 저작시 불편감을 주소로 내원하여 임상 구강 검사 결과 하악 우측 구치부의 scissor bite이 관찰되었다. 내원 당시 환아는 치과 치료에 대한 두려움과 거부감을 나 타냈고 이에 1년 동안 정기 검진을 하여 환자와의 신뢰관계를 형성 후 교정치료가 가능하였다. Williams Syndrome 환자의 경우 사교적이며 친밀한 성격임에도 치과종사자나 치과 치료에 대한 두려움을 가질 수 있어 치료를 시작하기 전 환자와 치과 종사자간의 관계 형성을 통한 신뢰를 획득함으로 더 나은 질의 치료를 시행할 수 있을 것이다.

요추 질환에 대한 신기공 오금희의 동작연구 - 20식, 30식, 40식을 중심으로 - (Study on the Movement of New Qi-gong "WuQinXi" Exercise for Lumbar Spinal Disease : Based on 20 Mode, 30 Mode, 40 Mode)

  • 유경곤;권영달;정현우
    • 동의생리병리학회지
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    • 제28권2호
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    • pp.129-136
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    • 2014
  • The "WuQinXi" exercise, one of the medical Qi-gongs, is an exercise maximizing human's self healing power and has been confirmed to be effective significantly at several modern researches. There are many exercise therapies in western medcine, such as Willams's flexion exercise, Mckenzie's extension exercise, vertebral stabilization exercise and so on. However, there isn't a special exercise therapy which can be applied for medical practice in oriental medicine. So we selected 24 motions which are related with lumbar movements from 3 type "WuQinXi" exercises ; 20 mode, 30 mode, and 40 mode. And then, we classified them according to lumbar movements as flexion, extention, lateral bending and rotation, and also functions as stabilization and rubbing. Next, with these classifications, we assorted them by kinds of lumbar spinal disease as HIVD(herniation of intervertebral disc), spinal stenosis, spondylolysis and spondylolisthesis, facet joint syndrome, compression fracture and spondylosis. We expect that "WuQinXi" exercise be a exercise therapy for lumbar spinal disease at an oriental medical clinic in this way. Oriental medical doctors will be able to teach easily patients "WuQinXi" exercise's motions at clinic, depending on kinds of lumbar spinal disease each patient suffers from. We plan to study the effect of "WuQinXi" exercise by comparing patients who do the "WuQinXi" exercise with the patients who do the western medical exercise therapy.