• Title/Summary/Keyword: Swyer syndrome

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Swyer-James(macleod's) Syndrome (Swyer-James(Macleod) 증후군)

  • 최영호
    • Journal of Chest Surgery
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    • v.27 no.11
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    • pp.970-972
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    • 1994
  • The Swyer-James syndrome is one of the very few condition that the density of one lung is markedly less than the density of the other and frequently presents a diagnostic problem. In 1989, we reported a case of Swyer-James Syndrome. Recently, we experienced a new case of this syndrome. Left upper lobectomy was performed and postoperative pneumonia was developed, but the patient was recovered.

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Bronchogenic Squamous Cell Carcinoma in Patient with Swyer-James Syndrome -One Case Report (Swyer-James (MacLeod) 증후군에 병발한 기관지원성 편평 상피세포암 1예)

  • 김경화;서연호;구자홍;김민호
    • Journal of Chest Surgery
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    • v.36 no.10
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    • pp.784-788
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    • 2003
  • Swyer-James syndrome is a rare disease with patients presenting with unilateral hyperlucent lungs and hypoperfusion due to hypoplasia of the pulmonary artery and bronchiolitis obliterans. A unilateral hyperlucent lung generally develops after a lower respiratory tract infection during early childhood. In extremely rare cases, an association of bronchogenic carcinoma with Swyer-James syndrome has been reported. We report a case of bronchogenic squamous cell carcinoma associated with Swyer-James syndrome that performed right upper lobectomy and lymph node dissection with a relevant literature review.

Swyer Syndrome: A Case Report (Swyer 증후군: 증례 보고)

  • Hyeong Gi Choi;Sohoon Park
    • Journal of the Korean Society of Radiology
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    • v.84 no.5
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    • pp.1181-1184
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    • 2023
  • Swyer syndrome is a rare form of primary amenorrhea resulting from gonadal dysgenesis. It is characterized by the presence of a female phenotype with a 46, XY karyotype. In our case, CT scans revealed the absence of the uterus and bilateral ovaries of the 16-year-old female patient. Calcific nodules were found in both inguinal areas, which were suspected to be calcified atrophic testes. A chromosomal study confirmed the diagnosis of Swyer syndrome. Herein, we report a rare case of Swyer syndrome.

Swyer-James (Macleods) Syndrome - One case report - (Swyer-James (Macleod) 증후군수술치험 1례)

  • 이헌재
    • Journal of Chest Surgery
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    • v.22 no.2
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    • pp.321-324
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    • 1989
  • The Swyer-James syndrome is rare abnormality that may be encountered on routine chest X * ray examination and frequently presents a diagnostic problem. Recently, we experienced a case of Swyer-James syndrome which was accompanied with ipsilateral uncontrolled pneumothorax. We performed exploratory thoracotomy because of failure of re-expansion of the lung. Right pneumonectomy was performed and postoperative course was uneventful.

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A Case of Bronchogenic Squamous Cell Carcinoma in Patient with Swyer-James Syndrome (Swyer-James 증후군에 병발한 기관지원성 편평 상피세포암 1예)

  • Park, Seoung-Ju;Jin, Heung-Yong;Choi, Bo-Geum;Choi, Koang-Ho;Lee, Heung-Bum;Lee, Yong-Chul;Rhee, Yang-Keun
    • Tuberculosis and Respiratory Diseases
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    • v.50 no.2
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    • pp.252-257
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    • 2001
  • Swyer-James syndrome is a rare disease with patients presenting with unilateral hyperlucent lungs due to hypoplasia of the pulmonary artery and bronchiolitis obliterans. A unilateral hyperlucent lung generally develops after a lower respiratory tract infection during early childhood. In extremely rare cases, an association of bronchogenic carcinoma with Swyer-James syndrome has been reported. Here we report a case of bronchogenic squamous cell carcinoma associated with Swyer-James syndrome with a relevant literature review.

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DENTAL TREATMENT OF A PATIENT WITH SWYER JAMES UNDER GENERAL ANESTHESIA: A CASE REPORT (Swyer James syndrome환아의 전신마취 하 치아우식 치료: 증례보고)

  • Sung, Young Jae;Song, Ji Soo;Hyun, Hong-Keun;Kim, Young-Jae;Kim, Jung-Wook;Jang, Ki-Taeg;Lee, Sang-Hoon;Shin, Teo Jeon
    • The Journal of Korea Assosiation for Disability and Oral Health
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    • v.15 no.1
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    • pp.60-64
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    • 2019
  • Swyer-James syndrome (SJS), also known as Swyer-James-MacLeod syndrome and unilateral hyperlucent lung syndrome, is rare acquired pulmonary disorder develops secondary to infectious etiologies in early childhood. Viral respiratory infection such as adenoviruses or Mycoplasma pneumoniae in infancy or early childhood rarely cause Swyer-James syndrome. It is generally characterized on radiographs by a unilateral small lung with hyperlucency and air trapping on expiration. In many cases unaffected lung tissue functions normally, compensating for affected lung portion. Preoperative assessment is needed to determinate individual's pulmonary function. A 4-year-old boy with Swyer-James syndrome visited Seoul National University Dental Hospital Department of pediatric dentistry for caries treatment. Clinical and radiographic examinations revealed multiple carious lesions on deciduous teeth. Considering patient's underling disease, age, and level of cooperation, dental treatment under general anesthesia was scheduled. Dental treatment was done with composite resin and stainless-steel crown. Since ventilation of Swyer-James syndrome patients was diminished because of airway obstruction, close monitoring of ventilation is necessary during dental treatment. Considering pulmonary pathology, general anesthesia rather than sedation is recommended when special behavior management is required for dental treatment. Swyer-James syndrome patients can tolerate general anesthesia and surgery well, according to several reports.

A Case of Swyer Syndrome Which showed a Positive SRY Gene in Peripheral Blood and Gonad (말초혈액과 생식선에서 SRY유전자 양성을 보인 Swyer증후군 1례)

  • Nam, Y.S.;Lee, S.H.;Han, J.H.;Cho, S.W.;Yoon, T.K.;Lee, C.N.;Cha, K.Y.
    • Clinical and Experimental Reproductive Medicine
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    • v.26 no.2
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    • pp.275-280
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    • 1999
  • Male sexual differentiation involves a cascade of events initiated by the presence on the Y chromosome of the of the SRY (sex determining region of Y chromosome) gene, which causes the indifferent gonad to develop into a testis. Hormonal products of the testis, predominantly testosterone and Mullerian inhibiting subtance (MIS), then control the sexual differentiation of the developing fetus. SRY is a transcription factor; however, target genes for its action have yet to be identified, because the DNA recognition sequence for SRY is found in many genes. Therefore the study of intersex disorders is being used to identify other genes active in the pathway of sexual differentiation. Patients with 46,XY gonadal dysgenesis, or Swyer's syndrome, have streak gonads, normal stature, and a sexually infantile phenotype with Mullerian structures present. The inheritance is usually sporadic but can be autosomal dominant or X-linked recessive. Unlike 45,X patients, stigmata of Turner syndrome are rare. As many as 20 to 30% of patients are at risk for malignant gonadal tumor formation and should undergo gonadectomy soon after the diagnosis is made. We have experienced a case of Swyer syndrome which showed a positive SRY gene in peripheral blood and gonad. So we report this case with a brief review of literatures.

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A case of pulmonary disease with unilateral hyperlucent lung (일측성 방사선 과투시성을 보인 폐질환)

  • Ohn, Joon-Sang;Seo, Jee-Young;Park, Mi-Ran;Rheu, Nam-Soo;Cho, Dong-Ill
    • Tuberculosis and Respiratory Diseases
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    • v.43 no.6
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    • pp.1042-1047
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    • 1996
  • The Swyer-James syndrome is a relatively uncommon disease entity presented with unilateral hyperlucent lung due to hypoplasia of a pulmonary artery and bronchiectasis of the affected lung. The main finding is a hyperlucent lung with small hilar shadows on the chest X-ray. Pulmonary angiography is the standard method for diagnosis. We report a case of the Swyer-James syndrome with a brief review of literature.

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A Case of Bilateral Spontaneous Tension Pneumothorax Associated with Mycoplasma pneumoniae Infection (Mycoplasma pneumoniae 폐렴에 동반된 양측 특발성 긴장성 기흉 1례)

  • Lee, Jae Won;Heo, Mi Young;Kim, Hae Soon;Lee, Seung Joo
    • Clinical and Experimental Pediatrics
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    • v.45 no.3
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    • pp.401-405
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    • 2002
  • Mycoplasma pneumoniae(M. pneumoniae) is the leading cause of pneumonia in school-age children and young adults. The clinical courses are usually mild but recently, severe cases were reported such as lung abscess, Swyer-James syndrome and adult respiratory distress syndrome. Spontaneous pneumothorax associated with M. pneumoniae infection is rare. Carlisle reported a 6-year-old patient with bilateral spontaneous pneumothorax associated with M. pneumoniae infection and Koura also reported a 18-year-old girl with repeated. M. pneumoniae pneumonia with recurrent pneumothorax. We experienced bilateral spontaneous tension pneumothorax and subcutaneous emphysema associated with M. pneumoniae infection in a 6-year-old boy who presented with dyspnea, chest pain, and neck swelling. We reported it as the first case in Korea.

A Case of Unilateral Hyperlucent Lung by Main Bronchus Obstruction (주가관지 폐쇄에 의한 일측정 방사선 과투과성을 보이는 1예)

  • Cho, Yong-Bum;Park, Kyeong-Soo;Jeon, Jeong-Bae;Ryu, Jeong-Seon;Moon, Tae-Hoon;Cho, Jae-Hwa;Kwag, Seung-Min;Lee, Hong-Ryeol;Cho, Cheol-Ho
    • Tuberculosis and Respiratory Diseases
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    • v.48 no.2
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    • pp.268-273
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    • 2000
  • A 32-year-old woman complaining of cough, sputum, and chest discomfort for the past ten days was admitted to the hospital. The radiologic findings were transradiant left lung with reduced number and size of vessels, mediastinal shifting to the right at expiration, matched ventilation-perfusion defect on ventilation-perfusion scan, and diffuse hypoplasia of the left pulmonary artery and i1s branches on the pulmonary angiography. We describe a case of unilateral hyperlucent lung by main bronchus obstruction in a patient who presents a clinical picture suggestive of the Swyer-James syndrome.

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