• 제목/요약/키워드: Subependymal giant cell astrocytoma

검색결과 3건 처리시간 0.021초

결절성 경화증에 동반된 상의하 거대 세포 성상세포종의 내시경적 수술 - 증 례 보 고 - (Endoscopic Surgery of a Subependymal Giant Cell Astrocytoma Associated with Tuberous Sclerosis - Case Report -)

  • 임정환;송준혁;김명현;박향권;김성학;신규만;박동빈
    • Journal of Korean Neurosurgical Society
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    • 제29권4호
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    • pp.564-568
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    • 2000
  • The authors present a rare case of subependymal giant cell astrocytoma which successfully treated with endoscopic tumor resection. A 15-year-old boy was presented with multiple episode of generalized seizure and intermittent headache for 5 years. The patient had facial adenoma sebaceum, multiple nevi on his back, and mental retardation. Cerebral MRI scans showed a round tumor located at the frontal horn of right ventricle near the foramen monro. The tumor was totally removed with endoscopic procedure and histologically confirmed as a subependymal giant cell astrocytoma. Subependymal giant cell astrocytomas can cause all the clinical problems that are associated with other types of intracranial tumor. However, surgical indication is not well standardized, because of the lack of basic knowledge about the tumor and the likelihood of surgical morbidity. We believe that endoscopic surgery, a minimally invasive technique, can circumvent the surgical disadvantage while achieving the surgical goal.

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결정성 경화증에서의 상의하 거대 성상세포종 (Subependymal Giant Cell Astrocytoma in the Tuberous Sclerosis)

  • 박진한;김성호;한동로;배장호;고삼규;김오룡;최병연;조수호
    • Journal of Yeungnam Medical Science
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    • 제11권2호
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    • pp.221-229
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    • 1994
  • 저자들은 발생 빈도가 드물고 상당한 크기의 상의하 거대 성상세포종을 동반하는 결절성 경화증환자에서 뇌량경유 접근법을 사용하여 좋은 결과를 얻었기에 보고하는 바이다.

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두피 및 사지에 다발성 섬유종을 동반한 결절성 경화증 (A Case of Tuberous Sclerosis with Multiple Fibroma on Scalp and Extremity)

  • 김형석;정희선;신극선;이상엽;송지선
    • Archives of Plastic Surgery
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    • 제35권3호
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    • pp.341-344
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    • 2008
  • Purpose: Tuberous sclerosis is an autosomal dominant multisystemic neurocutaneous syndrome characterized by the development of multiple hamartoma distributed through the body, skin, brain, heart, kidney, and lung. The classic triad is seizure, mental retardation, and facial angiofibroma. We experienced a case of a tuberous sclerosis associated with the facial lesion and multiple masses on scalp, forehead, and right lower extremity. Methods: This a 34-year-old male patient had subependymal giant cell astrocytoma in brain and multiple angiomyolipoma in both kidneys. Tangential excision with razor blade and dermabrasion were done on the centrofacial area. We excised other lesions and the mass on scalp was excised and covered with split thickness skin graft. Results: The histopathological finding revealed that the facial lesion was angiofibroma and the others were multiple fibroma. Conclusion: In our case of tuberous sclerosis, we chose the tangential excision to remove the large nodules of angiofibroma, and then dermabrasion was used to smooth the final contour. The patient appeared to have a good results from this treatment modality. But, tuberous sclerosis is an disease that needs long term follow-up to check up the recurrence of skin problem.