• Clinical and Experimental Pediatrics
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• 제56권11호
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• pp.500-504
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• 2013

Here we present the case of an 11-year-old female patient diagnosed with Caroli syndrome, who had refractory esophageal varices. The patient had a history of recurrent bleeding from esophageal varices, which was treated with endoscopic variceal ligation thrice over a period of 2 years. However, the bleeding was not controlled. When the patient finally visited the Emergency Department, the hemoglobin level was 4.4 g/dL. Transhepatic intrajugular portosystemic shunt was unsuccessful. Subsequently, the patient underwent percutaneous transhepatic variceal obliteration. Twenty hours after this procedure, the patient complained of aphasia, dizziness, headache, and general weakness. Six hours later, the patient became drowsy and unresponsive to painful stimuli. Lipiodol particles used to embolize the coronary and posterior gastric veins might have passed into the systemic arterial circulation, and they were found to be lodged in the brain, kidney, lung, and stomach. There was no abnormality of the portal vein on portal venography, and blood flow to the azygos vein through the paravertebral and hemiazygos systems was found to drain to the systemic circulation on coronary venography. Contrast echocardiography showed no pulmonary arteriovenous fistula. Symptoms improved with conservative management, and the esophageal varices were found to have improved on esophagogastroduodenoscopy.

• 대한영상의학회지
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• 제84권1호
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• pp.291-297
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• 2023

좌측 단독 문맥고혈압은 비장 정맥이 폐쇄되어 생기는 드문 임상 질환이다. 비장 정맥의 혈전증 혹은 외부 압박으로 인해 근위부 비장정맥의 고혈압이 발생하게 되며, 비장의 혈류는 짧은 위 정맥, 관상정맥, 위대망정맥 같은 측부혈관을 통하여 상장간막 정맥 혹은 문맥으로 흘러가게 된다. 위장관 출혈을 유발하는 좌측 단독 문맥고혈압에는 개복 비장절제술이 첫 번째 치료방법으로 추천된다. 하지만 중재시술을 통한 치료가 수술적 교정을 원치 않는 환자들에게는 임상적으로 유용한 치료 선택지가 될 수 있다. 본문에서는 위정맥류 출혈을 가진 좌측 문맥 고혈압에 대한 두 개의 증례를 다루고자 한다.