• Journal of Korean Neurosurgical Society
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• 제58권3호
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• pp.281-285
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• 2015

Myxomas are rare benign tumors that originate from mesenchymal tissue. They usually develop in the atrium of the heart, the skin, subcutaneous tissue, or bone. Involvement of the skull base with an intracranial extension is very rare and not well-described in the literature. We report a rare case of primary intracranial ossifying myxoma arising from the anterior skull base and mimicking a huge chondrosarcoma, and we review the relevant literature.

• Journal of Korean Neurosurgical Society
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• 제43권3호
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• pp.165-168
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• 2008

The location of ganglioglioma (GG) within the infratentorial compartment is unusual. The authors report a rare case of GG in the cerebellar hemisphere. A 12-year-old boy suffered from headache and gait disturbance. Neuroimaging studies demonstrated a large enhancing cerebellar mass with cystic components compressing the forth ventricle. After complete resection of the tumor, the patient became symptom free. Histological examination on the tumor disclosed glial cells and dysplastic ganglion cells. Although it is a rare tumor, in the appropriate clinical setting, a GG should be considered in the presence of a cerebellar mass with both solid and cystic components on magnetic resonance images in children.

• Investigative Magnetic Resonance Imaging
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• 제9권1호
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• pp.57-61
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• 2005

골육종은 주로 장골의 골간단 (metaphysic) 에 생기는 악성도가 매우 높은 종양으로 두개골에는 매우 드물게 생긴다. 저자들은 두개기저부에 생겨 접형골을 파괴시키면서 약 2개월 만에 재발한 골육종 1예를 보고하고자 한다. 두통과 어지러움증 그리고 오른족 볼쪽의 감각이 저하된 28세 남자의 전산화단층촬영과 자기공명영상소견에서 이 종양은 약 3cm 의 크기로 균일하게 조영증강이 잘 되면서 내부에 낭성변화가 동반된 소견을 보였다. 종양은 완전히 절제되었고 한달간의 항암요법을 시행하였다. 약 두 달후에 다시 시행한 자기공명영상 소견에서 처음 수술한 같은 부위에 다시 처음보다 크기가 더 큰 종양이 발견되었고 제 2차 수술후 병리소견에서 처음과 같은 골육종으로 확진되었다.

• Journal of Korean Neurosurgical Society
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• 제53권4호
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• pp.218-222
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• 2013

Objective : To clarify the anatomical correlations of the sphenoid sinus with surrounding structures in the normal Korean population, and to identify surgical landmarks for safe sellar floor dissection in the anterior skull base by endoscopy and microscopy. Methods : We reviewed the 196 brain magnetic resonance imaging findings showing a normal appearance, and measured the distances between anatomical landmarks. Results : The mean distances from the base of the columella to the anterior wall of the sphenoid sinus and the sellar floor were $69.71{\pm}4.25$ mm and $86.26{\pm}4.57$ mm, respectively in the over 15 age group, and showed the smallest degree of variation among the measurements. The mean angles between the floor of the nasal cavity and the straight line connecting the base of the columella and the sellar floor were $29.45{\pm}3.25^{\circ}$ and $24.75{\pm}4.00^{\circ}$ in the over 15 and under 15 age groups, respectively. The mean values of both distances and angles increased with age until 15 years after which no further increases were evident. There were no significant differences in the measurements between males and females or among subjects with different degrees of pneumatization in the over 15 age group. Conclusion : The distances from the base of the columella to the sellar floor and the anterior wall of the sphenoid sinus, which were consistent among individuals, could be used as a surgical indicator to investigate the sellar floor in endoscopic or microscopic transsphenoidal approaches.

• Investigative Magnetic Resonance Imaging
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• 제25권1호
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• pp.47-52
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• 2021

Paraganglioma is a rare tumor of paraganglia, derived from neural crest cells in sympathetic or parasympathetic ganglions. It can be widely distributed from the skull base to the bottom of the pelvis. The pancreas, however, is a rare location of this neoplasm, and only a limited number of cases have been reported in the English literature, especially with gadoxetic-acid-enhanced magnetic resonance imaging (MRI) and diffusion-weighted images (DWI). We herein report a case of pathologically proven paraganglioma in the pancreas head with a literature review on endoscopic ultrasonography (EUS), computed tomography (CT), gadoxetic-acid-enhanced MRI, and DWI sequence.

• Journal of Korean Neurosurgical Society
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• 제40권2호
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• pp.110-113
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• 2006

Surgery and radiotherapy are mainly used for plasma cell neoplasm which constitutes about $1{\sim}2%$ of human malignancy. The authors carried out Fractionated Stereotactic Radiotherapy[FSRT] on the residual tumor after the subtotal removal of Intracranial plasmacytoma. A huge mass lesion was observed on MRI [magnetic resonance image] in the left anterior and middle cranial fossa of a 63-year-old man with left exophthalmus which lasted for a month, and was suspected as a meningioma with strong contrast enhancement. Extramedullary plasmacytoma was diagnosed on histopathological examination. After the surgery, FSRT was also carried out on the residual tumor which invaded the skull base. One-year follow up after FSRT showed contrast enhancement only in the left sphenoid bone on MRI, which indicated significant decrease in the size of the tumor without any abnormal neurologic deficits. We treated intracranial plasmacytoma which invaded left anterior and middle cranial fossa and surrounded cavernous sinus without cranial nerve deficit through subtotal tumor removal and FSRT.

• 대한골관절종양학회지
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• 제11권1호
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• pp.94-99
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• 2005

부신경절종은, 신경외배엽 기원의 교감신경 신경내분비 세포로 이루어져 있는, 부신 이외의 부신경절에서 생긴 종양으로, 주로 갑상선, 목동맥체, 종격동, 폐, 십이지장, 대동맥 주변 부위와 후복막 부위에 잘 생긴다. 악성도는 조직학적인 진단에 의한 것이 아니라, 국소 림프절 재발과 원격 전이에 의하여 판별되며, 골 전이가 드물지만 전이가 일어나면 주로 두개골 기저, 척추에 생기며, 드물게 골반골, 대퇴골로 전이한다. 저자들은 대퇴부 피하층에 발생하여 혈관 기원성의 종양과 감별되었던 부신경절종과 조기 골 전이를 보인 후복막에 발생한 부신경 절종을 경험하여 문헌고찰과 함께 보고하고자 한다.

• Journal of Chest Surgery
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• 제38권11호
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• pp.799-802
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• 2005

랑거한스세포 조직구증식증은 호산구성 육아종, Letterer-Siwe병, Hand-Schuller 증후군을 포함하는 질환으로 이전에는 조직구증식증 X로 명명되어 왔다. 이 질환의 임상적 양상은 다양하며, 기본적인 종양의 성질은 양성이나 파종되는 성질이 아주 강하다. 질환의 자연 경과는 예측할 수 없다. 하지만, 뼈에 생긴 단일 병변일 경우 광범위 절제를 통해서 완치율을 높일 수가 있다. 대부분의 랑거한스세포 조직구증식증 환자에서는 주로 두개골 천정에 골용해 병변이 나타나며, 드물게 두개골 기저부와 대퇴골을 침범하기도 한다. 늑골에 생기는 단일 병소의 랑거한스세포 조직구증식증은 비교적 드물다. 본 저자들은 늑골에 생기는 단일 병소의 랑거한스세포 조직구증식증 2예를 외과적 절제술로 치료하였기에 보고한다.