• Title/Summary/Keyword: Perivascular epithelioid cell neoplasms

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Primary Perivascular Epithelioid Cell Tumor of the Lung: A Case Report

  • Hye Rim Na;Jong Hui Suh;Jiyun Lee
    • Journal of Chest Surgery
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    • v.56 no.5
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    • pp.367-370
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    • 2023
  • Perivascular epithelioid cell tumors (PEComas) are very rare mesenchymal neoplasms, composed of histologically and immunohistochemically distinctive cells that form a sheet-like appearance around vessel lumens. Although most are benign, a malignant subset does exist, complicating clinical diagnostic efforts. Proper evaluation and management are thus essential for long-term patient survival. Herein, we present a rare case of a benign pulmonary PEComa that was diagnosed postoperatively in a 45-year-old woman.

Angiomyolipoma of the Glabellar Region

  • Kim, Hyo Joong;Chung, Chan Min;Park, Jae Yeon;Jung, Sung Gyun
    • Archives of Craniofacial Surgery
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    • v.18 no.3
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    • pp.202-206
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    • 2017
  • Angiomyolipomas are hamartomatous lesions consisting of smooth muscle bundles, thick-walled blood vessels, and mature adipocytes. They are usually found in the kidneys of tuberous sclerosis patients and more rarely in other organs, such as the liver, the oral cavity, the sinonasal tract, the heart, the large intestines, the lungs, and the skin. Cutaneous angiomyolipoma has shown to be very rare and generally occurs at the ends of the digits, the elbows, the ears, and the nose. Herein, we report the first documented case of angiomyolipoma of the glabellar region.