• Title/Summary/Keyword: Ebstein's anomaly

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Ebstein's Anomaly -A Case Report- (엡스타인 심기형 -1례 보고-)

  • 전찬규
    • Journal of Chest Surgery
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    • v.27 no.1
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    • pp.57-59
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    • 1994
  • Ebstein`s anomaly, a rare congenital cardiac anomaly, is characterized by downward displacement of abnormal tricuspid valve. Indication for surgical repair and the optimal surgical approach are still controversy. Recently, we experience a case of Ebstein anomaly, which was treated by atrilized right ventricular plication and annuloplasty. The patient was discharged with good result on 17th post-operative day.

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Ebstein`s anomaly ; St. Jude Medical valve replacement using partial artificial annulus formation - A Case Report - (Ebstein 기형에 인공판윤을 이용한 금속형 St. Jude Medical 인공판막 대치술)

  • Lee, Jong-Guk;Jo, Jae-Min
    • Journal of Chest Surgery
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    • v.25 no.8
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    • pp.826-831
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    • 1992
  • Ebstein`s anomaly is characterized by a downward displacement of a malformed tricuspid valve, The ideal surgical management of Ebstein`s anomaly is not yet established. Recently we experience one case of Ebstein`s anomaly, which was treated sussessfully by partial artificial annulus formation, and tricuspid valve replacement with St. Jude Medical valve. We have achieved excellent results with mechanical valve replacement and partial artificial annulus formation using wessex pericardial patch. On follow up for 4 years, the patient is well and in functional class I.

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The Surgical management of Ebstein's anomaly: A Report of 4 cases of tricuspid valve replacement and plication of the atrialized right ventricle (Ebstein 심기형의 개심술 4례 (삼첨판막 대치이식술 및 우심실 Plication))

  • Im, Seung-Pyeong;Yang, Gi-Min;Lee, Yung-Kyoon
    • Journal of Chest Surgery
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    • v.13 no.4
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    • pp.435-441
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    • 1980
  • Ebstein`s anomaly had been amenable to reparative surgery since 1962. However, neither the role of surgery in Ebstein`s anomaly nor the surgical procedure of choice for its correction are clearly defined. Whether or not the atrialized right ventricle, which plays a major role in the functional abnormalities, should be obliterated in all cases remains unsolved. Four cases of Ebstein`s anomaly treated surgically at Seoul National University Hospital were reported. All had closure of the atrial septal defect, obliteration of the atrialized right ventricle by plication, and insertion of a tricuspid bioprosthesis and an epicardial ventricular pacemaker. One patient had a pulmonic valvotomy due to stenotic bicuspid pulmonic valve also. All but one had discharged with a good result.

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Surgical Treatment of Isolated Primary Tricuspid Insufficiency except Ebstein`s Anomaly - Report of 2 Cases - (Ebstein`s anomaly 이외의 격리성 원발성 삼천판 부전증[isolated primary tricuspid insufficiency]의 수술 치험 2례)

  • Baik, Hee-Jong;Ahn, Hyuk
    • Journal of Chest Surgery
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    • v.24 no.9
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    • pp.907-912
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    • 1991
  • Isolated primary tricuspid insufficiency except Ebstein`s anomaly is rare disease. Recently we experienced two cases of isolated primary tricuspid insufficiency and treated successfully with annuloplasty or valve replacement. We could not classify our case as one of the classification of isolated tricuspid insufficiency, because the morphology and microscopic finding did not suggest any similar variety.

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Cone Reconstruction for Tricuspid Valve Repair in a Patient with Ebstein's Anomaly - A case report - (Cone 재건술을 이용한 엡스타인 기형의 삼첨판막 성형술 - 1예 보고 -)

  • Lee, Cheul;Kwak, Jae-Gun;Lee, Chang-Ha
    • Journal of Chest Surgery
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    • v.42 no.4
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    • pp.509-512
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    • 2009
  • Ebstein's anomaly is a complex congenital defect of the tricuspid valve and right ventricle. Various surgical methods to repair the regurgitant tricuspid valve have been reported, and most of them depend on monocuspidalization with using the anterior leaflet. We report here on our first experience with Ebstein's anomaly in a 31-year-old female patient who underwent cone reconstruction of the tricuspid valve with using three leaflets.

Surgical Correction of Ebstein's Anomaly -11 cases- (Ebstein 기형의 외과적 치료 - 11례 -)

  • 이선희;김시훈;윤정섭;김치경;조건현;왕영필;곽문섭;김우찬
    • Journal of Chest Surgery
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    • v.29 no.11
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    • pp.1202-1206
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    • 1996
  • Ebstein's anomaly is an unusual and a rare congenital cardiac malformation but characteristic abnormality of the development of the tricuspid valve, right atrium and ventricle. The characteristic findings are a displaced tricuspid valve with a septal leaflet spiralling into the right ventricle. The surgical correction is variable and are left unsolved problem in surgical treatment of anomaly. Between January 1988 & December 1995, we experienced 11 cases of Ebstein's anomaly and associated cardiac anomalies are ASD, PFO, ASD with VSD. The typically displaced tricuspid valve leaflet was found in all cases. In the NYHA functional classification, three were in class II, seven were in class III, and one was in class IV. Nine patients were operated by tricuspid annuloplasty & plication with Danielson's method and two patients were done by tricuspid valve replacement with plication, and in all cases associated anomaly was corrected. Postoperatively, five patients suffered from complication - low cardiac output syndrome, arrhythmia and wound infection. There was no operative mortality and the postoperative courses were relatively good conditions with more improvement of symptoms.

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Ebstein`s Anomaly A Case Report of Plication and Tricuspid Annuloplasty (Ebstein 심기형 수술치험 1례 보고)

  • 이종수
    • Journal of Chest Surgery
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    • v.18 no.3
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    • pp.391-397
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    • 1985
  • Ebstein`s anomaly is a rare congenital cardiac malformation and characterized by downward displacement of an abnormal tricuspid valve cusps. But until now, the ideal surgical correction is still controversial. We present a case of Ebstein`s anomaly experienced lately. The patient was 13 year old girl with the complaints of dyspnea on exertion, fatigability and cyanosis. Echocardiography revealed downward displacement of septal leaflet of tricuspid valve and atrialized right ventricle. Cardiac catheterization and cineangiography revealed ASD and large right atrium. During operation, the atrialized right ventricle was plicated and tricuspid annuloplasty was done. And the two secundum type ASD`s were closed by direct suture closure. The patient`s postoperative course was uneventful and discharged on the 24th postoperative days.

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Surgical treatment of Ebstein`s Anomaly-Report of 6 cases- (Ebstein 기형의 외과적 치료-6례 보고-)

  • 왕영필
    • Journal of Chest Surgery
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    • v.20 no.3
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    • pp.506-511
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    • 1987
  • Increased clinical interest, stimulated by newer diagnostic techniques, has made it apparent that Ebstein`s anomaly represents a spectrum of right heart abnormalities. In the usual case, the septal and posterior leaflets of the tricuspid valve are not attached to the true annulus, but are displaced distally into the ventricle. Also the degree of malattachment and the structural deformities of the cusps may vary greatly. Recently we experienced 6 cases of Ebstein`s anomaly who underwent corrective operation in our hospital. Five patients were operated by plication and annuloplasty techniques based on the construction of a monocusp valve by the use of the anterior leaflet. Remained one was operated on by tricuspid valve replacement using No 31 mm C-E tissue valve. There was no operative mortality and the postoperative courses were relatively good with marked symptom improvement.

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Surgical Treatment of Ebstein`s Anomaly Report of a case (Ebstein 심기형의 개심술 1례)

  • Park, Guk-Yang;Lee, Jeong-Ho;Yu, Hoe-Seong
    • Journal of Chest Surgery
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    • v.18 no.3
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    • pp.436-439
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    • 1985
  • A patient of Ebstein`s anomaly underwent surgical repair on Oct. 24th, 1984. Tricuspid valve was replaced by 31mm St. Jude mechanical valve without plication of atrialized right ventricle. The annulus has been placed below the coronary sinus, with care not to damage the conduction system. But postoperatively complete heart block developed. Permanent pacemaker was implanted on his 12th POD. Now he has been followed up for 9 months. There was no hemodynamic problems yet.

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Surgical Treatment of Wolff-Parkinson-White Syndrome Combined with AV Nodal Reentrant achycardia in a Patient with Ebstein`s Anomaly - A report of one case - (Ebstein씨 심기형에 동반된 Wolff-Parkinson-White 증후군 및 방실결절 회귀성 빈맥에 대한 수술치험 1례 보고)

  • 장병철
    • Journal of Chest Surgery
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    • v.23 no.1
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    • pp.205-212
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    • 1990
  • A 17 year old female patient with Ebstein`s anomaly received surgical treatment for WPW syndrome and AV nodal reentrant supraventricular tachycardia[SVT] Electrophysiologic study revealed that an anomalous pathway was located in the right posterolateral portion and antegrade dual AV nodal pathway responsible for AV nodal reentrant tachycardia. The patient was underwent surgery on February 18, 1987. Intraoperative mapping was used to define the location of accessory pathway. The accessory pathway was cryoablated through the epicardium. Simultaneously discrete cryoablation around the perinodal area was performed to prevent AV nodal reentrant SVT. The atrialized right ventricle of Ebstein`s anomaly was plicated with 11 pledget mattress sutures under the cardiopulmonary bypass. Two and half years after surgery, the patient has no evidence of WPW syndrome or supraventricular tachycardia.

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