• 제목/요약/키워드: Congenital defect

검색결과 461건 처리시간 0.018초

심실 중격 결손증과 동반된 신생아 대엽성 폐기종 - 1례 보고 - (Infantile Lobar Emphysema with Ventricular Septal Defect -one case report-)

  • 김태호;김공수;구자흥;김민호
    • Journal of Chest Surgery
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    • 제32권1호
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    • pp.62-65
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    • 1999
  • 영아기 대엽성 폐기종은 다양한 정도의 호흡장애, 폐엽의 과팽창, 종격동의 이동, 폐 탈출등을 야기하는 신생아기 및 영아기에 발생하는 드문 질환이다. 원인은 대부분 특발성 이지만, 선천성 심장질환과도 관계가 있으며, 특히 좌우단락에 의한 폐동맥 고혈압과 밀접한 관계가 있다. 주로 호발하는 부위는 좌측 주 기관지, 좌측 상엽기관지, 우측 중엽 기관지이다. 본 증례는 우측 중엽 폐기종과 심실중격결손증이 동반된 2 주된 신생아로 심장수술 후에도 기계적인 호흡보조가 필요하였고, 우측 중엽 폐기종은 개선되지 않았다. 술후 7일째 우측 중엽 절제술을 시행하고 5일후 인공호흡기를 제거하였다. 환자는 술후 45 일째 좋은 상태로 퇴원하였다.

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Miniature Schunauzer Dog에서 발생한 심방중격 결손 증례 (A Case of Atrial Septal Defect (ASD) in a Miniature Schunauzer Dog)

  • 박철;최치봉;김일환;박희명
    • 대한수의학회지
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    • 제43권2호
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    • pp.307-310
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    • 2003
  • An atrial septal defect (ASD) is congenital heart disease with a communication between the atria, which allows blood to shoot from the atrium with pressure. A 3-month-old female Miniature Schunauzer was referred to the Veterinary Teaching Hospital of Konkuk University for the evaluation of systolic heart murmur. At presentation, the mucous membrane was cyanotic. On physical examination, an ejection-type systolic murmur was auscultated at the pulmonic area. In addition, thoracic radiography showed enlargement of main pulmonary artery and right atrial/ventricular enlargement. Echocardiography revealed dilated right atrium and atrial septal defect. However, mitral and tricuspid valve were still intact and well tolerating. The presence of an ASD was confirmed by identifying flow across the defect with color Doppler imaging. Doppler echocardiography provides a means of non-invasive documentation and quantification of ASD. Complete blood count and serum chemistry were not remarkable. Although large defect was confirmed between the two atrium, the patient did not show any obvious clinical signs of heart failure at this time.

심방중격결손증의 외과적 요법 (Surgical Treatment of Atrial Septal Defect)

  • 조형곤
    • Journal of Chest Surgery
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    • 제18권2호
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    • pp.174-181
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    • 1985
  • From Jun. 1980 to Mar. 1984, 33 cases of atrial septal defect, secundum type, operated at the department of Thoracic and Cardiovascular Surgery, School of Medicine, Keimyung University, were analyzed retrospectively. They were 24.3% of all congenital heart diseases operated in the same period. Among the 33 cases, 17 cases were males and 16 cases were females. Their ages were ranged from 4 to 42 years and cases of over 15 years of age were 60.6%. Main symptoms at admission were exertional dyspnea [69.7%], palpitation [63.6%] and frequent upper respiratory infections [51.5%], but 2 cases [6.1%] were asymptomatic. All 33 cases were operated under the direct vision with cardiopulmonary bypass. All cases were secundum type defect of atrial septal defect and single defect were in 29 cases [90.6%], and oval type defect were in 31 cases [96.9%]. In 7 cases [21.9%], other lesions of cardiovascular system were associated, and the most common lesion was pulmonic valvular stenosis [4 cases; 12.5%]. The defects were closed directly in 27 cases and in 6 cases with Dacron patch. Postoperative complications were occurred in 8 cases [24.2%], and they were pleural effusion, congestive heart failure, and alopecia mainly. One case died due to air embolism postoperatively and operative mortality was 3.1%.

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심실중격결손의 Pulmonary Banding: 2 치험례 (Pulmonary Artery Banding for Ventricular Septal Defect: Report of 2 Cases)

  • 조범구
    • Journal of Chest Surgery
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    • 제5권1호
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    • pp.29-34
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    • 1972
  • Interventricular Septal Defect is probably the most common congenital cardiac lesion. Despite rapid technical advances and increasing surgical experience the risk of surgical intervention for correction of Ventricular Septal Defect in infants with pulmonary hypertension remains formidable. Since Sirak et al [1959] reported a succesful case of two stage approach to their surgical correction, it has led to a policy of primary palliation,followed by complete correction as a secondary procedure, after age 3 to 4 years. Most surgeon prefer to perform complete correction of Ventricular Septal Defect when body weight exceeds 30 Lbs. and before development of so-called Eisenmengers complex, for the good postoperative results. Authors report 2 cases of Ventricular Septal Defect with pulmonary hupertenslon, who was underwent pulmonary artery banding as a palliative procedure in the Department of Surgery,Severance Hospital Yonsei University. Case 1:4 year old male, initially a complete correction of Ventricular Septal Defect was attempted by the help of mild hypothermia and extracorporeal circulation. During the procedure of a construction of an extracorporeal by- pass, a sudden cardiac arrest developed. After resuscitation of the heart,pulmonary artery banding was performed as a palliation. On the first postoperative day the patient developed generalized tonic convulsion, cyanosis, vomiting and eventually shock. Patient discharged home after a full recovery. Case 2.: 9 month old female, the pulmonary artery constricted with Teflon patch successfully. After the patients first postoperative day several cyanotic spells developed followed by 3 cardiac arrests. This repeated until when she expired with respiratory failure.

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Partial anomalous pulmonary venous connection with intact atrial septum in a child with ventricular septal defect: a case report

  • Kim, Young-Nam;Cho, Hwa-Jin;Cho, Young-Kuk;Ma, Jae-Sook
    • Clinical and Experimental Pediatrics
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    • 제55권1호
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    • pp.24-28
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    • 2012
  • Partial anomalous pulmonary vein connection (PAPVC) is a rare congenital abnormal cardiac defect involving the pulmonary veins draining into the right atrium (RA) directly or indirectly by venous connection. Ninety percent of PAPVCs are accompanied by atrial septal defect (ASD). To our knowledge, there is no previous report of PAPVC with ventricular septal defect (VSD) without ASD in Korea, and in this paper, we report the first such case. A 2-day-old girl was admitted into the Chonnam National University Hospital for evaluation of a cardiac murmur. An echocardiogram revealed perimembranous VSD without ASD. She underwent patch closure of the VSD at 5 months of age. Although the VSD was completely closed, she had persistent cardiomegaly with right ventricular volume overload, as revealed by echocardiography. Three years later, cardiac catheterization and chest computed tomography revealed a PAPVC, with the right upper pulmonary vein draining into the right SVC. Therefore, correction of the PAPVC was surgically performed at 3 years of age. We conclude that it is important to suspect PAPVC in patients with right ventricular volume overload, but without ASD.

선천성 심장질환을 가진 영아에서 발견된 폐 격리증을 동반하지 않은 폐의 이상 체 동맥 기시 1례 (Anomalous systemic arterial supply to lung without sequestration in an infant who has congenital heart disease : a case report)

  • 장연우;최덕영
    • Clinical and Experimental Pediatrics
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    • 제49권8호
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    • pp.895-897
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    • 2006
  • 폐 격리증이 없는 정상적인 폐에 체 혈관이 이상 기시하는 것은 매우 드문 질환이다. 저자들은 반복적인 하기도 감염을 보이는 영아에서 선천성 심장질환의 상태가 본 하기도 감염을 나타낼 정도로 심하지 않음을 이상히 여겨 컴퓨터 단층 촬영을 시행하였다. 그 결과 폐 격리증이 없는 폐의 이상 체 동맥 기시가 우측 폐하 엽에 존재함과 동시에 우측 하엽 폐동맥이 없는 사실을 확인하게 되었다. 어린 나이에 이 같은 선천성 질환의 조합은 이전에 보고 된 바가 없는 매우 드문 질환으로 생각된다.

술후 심전도 변화가 예후에 미치는 영향에 관한 고찰 -선천성 심질환을 중심으로- (The prognostic implication of postoperative ECG changes in congenital heart surgery)

  • 정황규
    • Journal of Chest Surgery
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    • 제19권3호
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    • pp.363-373
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    • 1986
  • Even though the pathogenesis is still controversial, electrocardiographic changes after congenital open heart surgery depend on various etiologic factors. Author reviewed 261 cases of congenital open heart surgery patient experienced in the Dept. of Thoracic & Cardiovascular Surgery, Pusan National University Hospital, since July, 1981 to Sept., 1985. The results were summarized as followed: 1. The age distribution was from 3 to 29 years old with mean age 10.8 years. And the most frequent congenital heart defect we had done operation was VSD. 2. Preoperatively, the most frequent ECG finding was abnormal QRS complex and postoperatively the most frequent ECG change was arrhythmia. 3. The most frequent arrhythmia before operation was intraventricular conduction disturbance. 4. Right ventriculotomy incision produced the more frequent abnormal ECG changes postoperatively than right atriotomy or pulmonary arteriotomy. 5. According to the operative technique, outflow patch graft of TOF repair produced the highest frequency of ECG changes after operation, and in comparing simple and patch closure of VSD, the latter was higher frequency of ECG changes, in valvotomy and infundibulectomy of PS, the latter was higher too. 6. The common symptom and signs in abnormally ECG changed patients after operation were palpitation, dyspnea, congestive heart failure and murmur in this order., 7. The longer the time of CPB, the more number of abnormally ECG changed patients had been developed after operation. 8. The most of postoperative ECG changed patients recovered spontaneously or with only medication and were clinically insignificant. And the rest other minor group recovered with temporary pacing. Eight cases out of 261 [3.1%], these with abnormal QRS complex and arrhythmia couldn`t recover in spite of every effort and eventually succumbed.

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성인의 선천성 심질환;122례 분석 (Congenital Heart Disease in the Adult - 122 Cases Analysis -)

  • 정신현
    • Journal of Chest Surgery
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    • 제25권7호
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    • pp.769-776
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    • 1992
  • Total 632 cases of open heart surgery were performed in the department of thoracic and cardiovascular surgery, Pusan Paik Hospital, Inje University from october 1985 to december 1990. Among them, there were 503 cases of congenital heart disease and 129 cases of acquired heart disease. In the cases of 503 congenital heart disease surgically corrected, 122 cases over 15 years of age were reviewed and its results were summarized as follows ; l. In total 122 cases 65 were male and 52 female. 2. There were 54 patients under 20 years of age, 31 between 20 & 24 years, 20 between 25 & 29 and 17 over 30 years of age. The eldest was a 46-year-old female of atrial septal defect group. 3. There were 63 cases of VSD[51.7%], 38 of ASD[31.2%], 11 cases of TOF[9%] and so on. 4. In recovery cases, main post-operative complications were as follows; cardiac tamponade, arrhythmia, low cardiac output syndrome, pulmonary, edema pericarditis, mediastinitis, sepsis and DIC. 5. There were 3 cases of post-operative death in this series, so operative mortality rate was 2.5% compairing with 1.8% of pediatric cases below 15 years of age. 6. This reviewed series reveal that aggressive surgical approach in adult congenital heart disease can be justified with low operative mortality like as pediatric age group.

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흉강경을 이용한 우측 선천성 횡격막 탈장 수술 -1예 보고- (Thoracoscopic Repair of a Right-sided Congenital Diaphragmatic Hernia -A case report -)

  • 조태준;이재웅;이원용;홍기우;안수민;김건일
    • Journal of Chest Surgery
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    • 제40권2호
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    • pp.155-158
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    • 2007
  • 선천성 횡격막탈장은 신생아기에 응급 수술을 요하는 질환으로 주로 좌측에 많이 발생한다. 우측 선천성 횡격막 탈장은 드물며 증상이 경미하여 신생아기 이후에 발견되는 경우가 많다. 치료는 전통적으로 개흉술을 통한 횡격막 봉합술이 시행되지만 흉강경을 이용한 수술이 적용되어 좋은 결과들이 보고되고 있다. 우리는 우측 선천성 횡격막 탈장을 가진 5개월된 여아를 흉강경을 이용하여 수술하였기에 보고하는 바이다.

심방중격 결손증에 대한 임상적 고찰 (Clinical Studies of Congenital Atrial Septal Defects - A Case Report -)

  • 조용준;오봉석;이동준
    • Journal of Chest Surgery
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    • 제25권4호
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    • pp.383-390
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    • 1992
  • From Oct. 1983 to Dec. 1991, 135 cases of atrial septal defect which were operated at the department of Thoracic and Cardiovascualr Surgery, Chonnam National University Hospital, were analysed retrospectively. They were 23.7% of all congenital heart diseases operated in the same period. Among the 135 cases, 62 cases were male and 73 cases were female. Their ages were ranged from 2 to 54 years and the mean was 18 years old. Main symptoms at admission were exertional dyspnea[70.37%], frequent URI[49.12%] and palpitation[32.59%], but 12 cases[8.88%] were asymptomatic. Electrocardiographic findings wer regular sinus rhythm in 96.99%, RVH in 64.66%, incomplete RBBB in 27.06%, complete RBBB in 42.10%, and first degree AV block in 9.02% All 135 cases were operated under the direct vision with cardiopulmonary bypass. Anatomically, most frequent type was fossa ovalis defect with complete septal rim[78.52%]. 117 of 135 ASD patients were repaired with pathch closure[86.66%] and 14 patients were repaired with direct closure[10.37%] and 4 patients in mutiple ASD were repaired with patch and direct closure[2.96%]. Postoperative complications were occured in 21 cases[15.56%], and they were wound infection, pleural effusion, postoperative bleeding, urinary tract infection, and heart failure mainly. One case died due to epidural hematoma and operative mortality was 0.74%.

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